Cerebromedullary malformation ciwo

Arnold-Chiari ciwo ne mai tsanani nakasar anomaly na shugaban da mutum kwakwalwa. Its ainihi ta'allaka ne da fidda tsakanin size of na baya fossa da kwanyar, da kuma wasu a cikin wannan yankin na kwakwalwa Tsarin. Wannan take kaiwa zuwa tsallake bi ƙeta tonsils cerebellum da kwakwalwa kara. A mita na wadannan anomalies ne 4-8 lokuta da kowane 95-100 dubu. Man.

A halin yanzu, da pathogenesis da cuta ne bai tabbata ba. Mai yiwuwa, akwai uku pathogenic dalilai taimakawa wajen wannan cuta:

1. nakasar, hereditary neuropathy.
2. traumatic rauni sandan-sandan-occipital da kuma gasa rabo gangara a sakamakon wata haihuwa rauni.
3. CSF hydrodynamic buga a kan bango na laka canal, dake a cikin cibiyar.

hudu iri anomalies aka kasaftawa a 1891 Arnold Chiari, yi amfani da wannan rarrabuwa zuwa yau.

Arnold-Chiari ciwo irin ne shafewa na baya fossa kwanyar da kewaye Tsarin a cikin kashin baya canal ne da yawa m fiye da matakin da foramen magnum. A karo na biyu da irin anomaly ne ba caudal sāke wuri na medulla oblongata, da ƙananan sassa na tsutsa da IV ventricle, da kuma quite sau da yawa ci gaba hydrocephalus. Arnold-Chiari ciwo ne na uku irin ne sosai rare, domin shi ne halin da m biya diyya duk kwakwalwa Tsarin daga cikin na baya fossa. A karo na hudu irin aka wakilta cerebellar hypoplasia. A karo na hudu da kuma na uku iri anomalies a mafi yawan lokuta, m da rai.

A 80% na lokuta, Arnold-Chiari ciwo ne kamu da syringomyelia - Pathology na laka halin da ci gaban cysts na laka, wanda aka kafa ta shafewa na baya fossa matsawa da kwanyar da mahaifa yankin na laka. A gaban wadannan cysts take kaiwa zuwa cin gaban m myelopathy.

Arnold-Chiari ciwo: Alamun

The asibiti hoto na cutar halin da wadannan cututtuka:

• zafi a cikin wuyansa, kuma occipital yankunan, wanda qara lokacin sneezing ko tari.
• ragewan da yawan zafin jiki da kuma zafi ƙwarai, kazalika da babba wata gabar jiki tsoka ƙarfi.
• reshe spasticity.
• dizziness, aka rufe da mãgãgi, unsteadiness, aggravated ta juyo da kanka, rage gani acuity da kuma ingancin hangen nesa.

A sosai mai tsanani lokuta bayyanar cututtuka tsara a layi to wadannan gajere lõkacin fatara daga numfashi (apnea), da weakening na pharyngeal reflex da kuma m, involuntary ƙungiyoyi daga cikin idanu.

A wasu lokuta, Arnold Chiari anomaly iya ba da wani bayyanar cututtuka da kuma aka samu gaba daya kwatsam a lokacin bincike hanyoyin. Ganewar asali na cutar da ake za'ayi amfani MR Dabarar kuma lissafta tomography tare da uku-girma maimaitawa na mahaifa vertebrae, kuma occipital kashi.

Arnold-Chiari ciwo: Jiyya

Sanya lura dogara a kan haƙuri, kuma mai tsanani daga cutar. A cikin wadannan farko bayyanar cututtuka kamar ciwon kai da kuma sauran iri zafi, your likita iya bayar da shawarar zafi magani da kuma na yau da kullum rajistan shiga-rubucen. Wasu marasa lafiya ruwaito taimako a lokacin da shan anti-mai kumburi da kwayoyi da cewa zai iya hana ko jinkirta wani aiki.

Mafi sau da yawa, magani, likitoci fi son ciyar munanan surgically. The aiki ne don dakatar da ci gaban da canje-canje na kashin baya da kuma kwakwalwa tsarin da kuma karfafawa daga cututtuka. Lokacin dauke da fitar da wani cin nasara m vmeschatelstva muhimmanci rage-rage matsa lamba a kan laka da cerebellum, kazalika da murmurewa da CSF outflow. Akwai daban-daban dabaru na yadda ake gudanar da suke dogara da ciwon hydrocephalus. A talakawan duration na tiyata ne daya da rabi zuwa biyu hours, da dawo da lokacin daukan biyar zuwa bakwai kwanaki.