Kiwon lafiyaCututtuka da kuma Yanayi

Gunther cuta - abin da yake da shi?

Akwai zamani masana kimiyya suka tsanani yi imani da cewa dukan labarun da Vampires da kimiyance. Suna iya zama a ƙarƙashin rinjayar da irin wannan rare cuta kamar yadda wata cuta Gunther ko "cutaneous porphyria." Wannan cuta ya turbuɗe da jini, samar da disturbances a cikin haifuwa na dutse mai daraja. An yi imani da cewa Gunther ta cuta ya fi na kowa a cikin kananan kauyuka na Transylvania. Akwai shi ya taso ne daga cikin hankali da alaka da ãyõyinMu.

Masana sun ce idan ba don wannan cuta, ba za su taba samun wani labaru da tatsuniyoyi na Vampires, Dracula da sauran heroes da fangs. Kusan duk asymptomatic haƙuri wanda ya fara karfi Gunther ta cuta - hankula vampire fina-finai.

Nemo dalilin da matsala, kuma don bayyana cutar iya kawai a cikin karni na 20th. Kafin wannan da aka kwashe a real yaki tare da Vampires: daga 1520 zuwa 1630 a Faransa kadai kashe fiye da dubu 30 mutane, wanda aka dauke Vampires. A zurfi a cikin ƙasa zo ta hanyar Kristanci, da kuma da ruthlessly bi da mutanen da suka rinjãya a makara cutaneous porphyria.

Daga wannan rare nau'i na kwayoyin cuta sha daya kawai mutum da 200 da dubu. A wannan yanayin, idan irin wannan matsalar yana fama da daya daga cikin iyaye, sa'an nan ba za mu iya magana game da wani 25% yaƙĩni da cewa Günther ta cutar bayyane da yaron.

An yi imani da cewa wannan cuta - sakamakon lalatar. Medicine ya bayyana game da 80 lokuta da m porphyria a lokacin da ba shi yiwuwa in warkar. Gunther ta cutar halin da cewa jiki ba ya nuna babban aka gyara daga jini - ja jini Kwayoyin. Kuma wannan da aka nuna a cikin rashin baƙin ƙarfe da oxygen a cikin jini.

A cikin tsokoki da kuma jini ne da wani take hakkin pigment metabolism kuma saboda hasken rana fara rarrabu haemoglobin. Bugu da kari, wannan tsari ya auku agara iri da take kaiwa zuwa curling na yatsunsu a wasu lokuta.

Gunther ta cutar halin da cewa da duwatsu masu daraja (maras gina jiki na haemoglobin) an canza kama zuwa wata mai guba abu, wanda zai iya corrode da subcutaneous nama. Saboda wannan, da fata ya zama ruwan kasa a launi, thins da kuma karya bayan shi amsa hasken rana. A saboda wannan dalili, a kan lokaci fata ne rufe gaba daya da sores kuma scars. Bugu da kari, da kumburi lalata kunnuwa da hanci, mai tsanani deforming su.

Tunanin wani mutum da nada yatsun kafa da fuska rufe sores ... Yake ban tsoro? Irin wannan marasa lafiya kawai contraindicated hasken rana, saboda shi ya kawo su girma wahala. Fata, located a kusa da gumis da lebe tsaurara da kuma bushe. Saboda wannan saukar zuwa gumis fili incisors, samar da wani m vampire grin.

Wani alama da wannan cuta: hakora dakatarda porphyrin, saboda wannan dalilin, ba za su iya saya ja ko m-kasa-kasa launi. A haƙuri yana da sosai kodadde fata murfin. A rana suka ji karfi lethargy da kuma rashin makamashi, samar da makamashi da aka koma kawai a dare. Shi ne ya kamata a lura cewa dukan sa na bayyanar cututtuka halayyar kawai na marigayi mataki cuta. Akwai sauran, da yawa kasa m nau'i na porphyria.

Har sai da na biyu da rabi na karni na 20th, Gunther cuta da aka dauke kusan m. Akwai shaida da cewa a tsakiyar zamanai, don sauƙaƙe haƙuri da yanayin da ya aka bai sabo jini zuwa cika rashin jini Kwayoyin. Babu shakka, wannan bai bayar da wani sakamakon, saboda ingantattun jihar na jini, kamar shan ta rabo, ba shi yiwuwa.

Marasa lafiya da porphyria ba zai iya ci tafarnuwa, saboda acid, wanda aka fito da wannan kayan lambu, ƙaruwa sakamakon cuta lalacewa. Cuta porphyria zai iya sa artificially, ta amfani da wasu poisons da kuma sunadarai.

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