Kiwon lafiyaCututtuka da kuma Yanayi

Interstitial cutar huhu: description, haddasawa, cututtuka, ganewar asali, rarrabuwa da kuma magani

Menene interstitial cutar huhu? Jiyya daga cikin wadannan cututtuka, su bayyanar cututtuka da kuma rarrabuwa za a iya bayyana a baya.

Takaitacciyar

Interstitial cutar huhu - shi ne wani hadadden kullum cututtuka na huhu nama da bayyana kumburi da kuma capillary endothelial take hakkin tsarin perivazalnyh alveolar ganuwar da perilymphatic kyallen takarda. A halayyar alama na wannan pathological yanayin ne dyspnea. Wannan alama ne a gani na huhu insufficiency.

Interstitial cutar huhu sau da yawa kai ga fibrosis. A zamani likita yi, wannan lokaci ba a yi amfani da matsayin dangantawa ILD, amma wani lokacin har yanzu amfani da wannan ma'ana.

rarrabuwa

A kan me ya bambanta interstitial cutar huhu? A rarrabuwa na wadannan cututtuka na faruwa a kan etiological tushen:

  • Reaction kwayoyi, ko kuma wajen, to maganin rigakafi, antiarrhythmic kwayoyi da kuma kwayoyi domin jiyyar cutar sankara.
  • Inhalation na wasu abubuwa daga cikin kewaye matsakaici (inorganic da kwayoyin abubuwa, silicosis, berylliosis, asbestosis, rashin lafiyan alveolitis exogenous ko Hypersensitivity pneumonitis).
  • Tsari connective nama cututtuka (rheumatoid amosanin gabbai, scleroderma, tsari lupus erythematosus, dermatomyositis).
  • Idiopathic (histiocytosis X, sarcoidosis, alveolar proteinosis, idiopathic na huhu fibrosis, idiopathic interstitial alveolitis, ciki har da m interstitial alveolitis).
  • Kamuwa (Pneumocystis ciwon huhu, SARS, da tarin fuka).
  • Associated interstitial cutar huhu (tare da hanta cututtuka: primary biliary cirrhosis, aiki kullum hepatitis, da na huhu vasculitis: lymphomatoid granulomatosis, Wegener ta granulomatosis, Hypersensitivity vasculitis, necrotizing vasculitis, tsari; a "dasa a kan rundunar" dauki).
  • M marurai (carcinomatosis limfangitny).

Menene ILD?

Kamar yadda aka ambata a sama, da interstitial cutar huhu ne da Generic sunan Airways cuta kungiyar. Suna da, a kowa ne cewa su duk shafar interstices, cewa shi ne wani ɓangare daga cikin huhu.

Interstitial connective nama kira na huhu nama. Yana bayar da goyon baya ga microscopic iska sacs da Alveoli daga cikin huhu.

Jini wucewa ta cikin interstitium aiki gas musayar aiki tsakanin iska a cikin numfashi fili da kuma jini. Interstitial nama ne sai bakin ciki da cewa shi ne, ba a bayyane a kan x-ray ko a lokacin CT. Amma, duk da wannan, shi ne har yanzu a cutar za a iya gano a cikin shakka daga wadannan bincike.

Duk wani huhu nama cututtuka sa ta thickening. Irin wannan pathological yanayin na iya haifar da daga kumburi, kumburi ko scarring. Wasu iri rauni interstitial nama wuce da sauri, yayin da wasu ne m ko na kullum.

Sanadin cutar

Me ya sa ni ina da ciwon interstitial cutar huhu (magani shawarwari na masana za a gabatar a kasa)? Akwai su da yawa daban-daban Sanadin huhu nama raunuka. Alal misali, interstitial ciwon huhu lalacewa ta hanyar ƙwayoyin cuta, kwayoyin ko naman gwari. A ci gaba da sauran cututtuka iya hade tare da na yau da kullum inhalation na irritants kamar asbestos, talc, silica ƙura, karfe turɓãya, ci ko hatsi. Sosai da wuya huhu cututtuka na wannan kungiya suna kafa saboda da sakamakon narcotic aka gyara.

A fasalin da ILD ne cewa duk wadannan dalilai taimaka ga ci gaban da wasu cutar. A mafi yawan lokuta haddasawa kasance ba a sani ba.

cuta cututtuka

Yaxuwa interstitial cutar huhu halin da kumburi da huhu da nama da kuma ta m lalacewa. Irin wannan pathological jihohin tare da nakasa daga 'ya'yan numfashi. Wannan shi ne babban alama na ILD. A farko, shortness na numfashi ne ba ma m, amma yana da daraja da haƙuri yi darasi ko hawa matakala, ta nan da nan da ke sa kansa ji.

Ya kamata mu ma lura cewa ga ILD halin da bushe tari. Har ila yau, marasa lafiya rasa nauyi muhimmanci. Bã su da wani hadin gwiwa da kuma tsoka zafi, gajiya. A ci-gaba lokuta, mutum ya abnormally kumbura kusoshi, lebe da kuma fata juya blue. Irin wannan pathological sabon abu hade da low matakan da oxygen a cikin jini.

Ganewar asali interstitial huhu cututtuka

Yadda za a gane cutar karkashin shawara? Kamar yadda mai mulkin, mutane da ILD pulmonologist gunaguni da tari, kuma shortness na numfashi. Don yin daidai ganewar asali, likita yawanci amfani da wadannan haske hanyoyin:

  • Lissafta tomography. Ta wannan hanya, za ka iya ƙirƙirar wani cikakken image na huhu, kazalika da dukan m Tsarin. ILD fairly sauƙi kamu da CT.
  • X-ray. Irin wannan nazarin daga cikin kirji da aka saba yi don tantance janar yanayin na huhu tsarin. Shafi interstitial bayyana a images a cikin nau'i na lafiya Lines.

  • Babban ƙuduri CT. Daidai na'urar daukar hotan takardu saituna, kazalika da masu sana'a kwarewa muhimmanci ƙara da bincike inganci na ILD.
  • Huhu biopsy da kuma nazari na samfurori karkashin wani hange. Popular sau da yawa shi ne kawai hanya domin sanin ko irin lalacewar huhu nama. Its samfurori za a iya dauka amfani Videoassisted thoracoscopic tiyata, bronchoscopy ko toraktomii.

Ya kamata kuma a lura da cewa, ga kimantawa na numfashi aiki , wasu masana gudanar da gwaje-gwaje na musamman, ciki har da spirometry, jiki plethysmography, da sauransu.

Magani da kuma na asibiti da jagororin

Interstitial cutar huhu - wannan shi ne quite wani tsanani cuta bukata nan da nan magani. A makirci na lura da irin cututtuka ya kamata a zabi kawai pulmonologist, dangane da hanyar ci gaba da kuma nau'in nama lalacewa.

A mafi yawan lokuta, magani da aka yi da ILD maganin rigakafi. Irin wannan jamiái ne tasiri ga da yawa iri interstitial ciwon huhu na kwayan asalin.

Amma kwayar ciwon huhu, kamar yadda mai mulkin, shi gudanar da kansa. Bi da shi tare da maganin rigakafi ake bukata. Ya kamata kuma a lura cewa wannan rare cuta, duka biyu fungal ciwon huhu, da aka shafe kawai ta hanyar takamaiman antifungal jamiái.

Wani irin magani da ake amfani da magani daga ILD ne corticosteroids. Irin shirye-shirye kashe kumburi, ba kawai a cikin huhu, amma kuma a wasu sassa na jiki. Af, wasu jamiái amfani domin lura da cutar a tambaya zai iya kawai rage gudu da lalacewar da huhu, kazalika da tabarbarewar aikinsu. Har ila yau, sau da yawa suka kashe da na rigakafi da tsarin rage kumburi, wadda take kaiwa zuwa wasu kiwon lafiya matsaloli.

Mutane da low oxygen abun ciki a cikin jini tsarin, masana shawara numfashi oxygen ta musamman na'urorin. Wadannan hanyoyin za su taimaka wajen inganta harkokin yanayin haƙuri, kazalika da cika da bukatar na zuciya tsoka a cikin Yã 2.

Ya kamata mu ma lura cewa likitoci da shawarar da marasa lafiya faru a wasu lokuta, a huhu dashi. Wannan shi ne sau da yawa da mafi inganci Hanyar tafiyad da cuta, musamman a cikin tsanani, kuma m lokuta.

Outlook

Wasu marasa lafiya a kan bango na ILD tasowa zuciya rashin cin nasara, kuma akwai hawan jini a cikin huhu tasoshin. A chances na haƙuri ta dawo ko worsening cuta shakka dogara ne a kan dalilai na su ci gaba, mai tsanani da kuma ganewar asali lokaci. Ya kamata a lura cewa idiopathic na huhu fibrosis ne fairly matalauta hangen nesa.

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