Kiwon lafiyaCututtuka da kuma Yanayi

Subleukemic myelosis - da benign bambance-bambancen da kullum da cutar sankarar bargo

Subleukemic myelosis ne daya daga wani rukuni na jinkirin kullum cutar sankarar bargo, inda cikin hanyar cutar zama pathological canji precursor Kwayoyin myelocyte. Lokaci guda tare da mai illa maturation na hematopoietic Kwayoyin a wannan cuta tsari ɓullo da amsawa fibro-sclerotic raunuka a ƙasusuwan kwarangwal tare da concomitant matsawa da bargo da kuma proliferative canje-canje a cikin baƙin ciki da kuma hanta. Wannan shi ne dalilin da ya sa subleukemic myelosis ake magana a kai a matsayin myeloproliferative cutar sankarar bargo.

Dalilan myelofibrosis da kuma bambance-bambancen karatu da cutar

A mafi yawan lokuta, cutar ta auku a cikin marasa lafiya da suke da shekaru 50 da mazan, sai wani daraja a haɗe zuwa kayyade matsalar aiki na samfur na nukiliya abu kara progenitor Kwayoyin, autoimmune cuta, kwayar cututtuka. Morphological substrate zama mieloza canza duka uku jam hematopoiesis - granulocytic, megakaryocytic da erythroid. Yana da har zuwa mai tsanani daga wadannan cuta da kuma dogara da cutar da kuma hangen nesa.

A mafi yawan lokuta subleukemic myelosis Saide wajen benign, kuma akwai wani kai tsaye hulda a tsakanin haƙuri shekaru a lokacin da farko na cutar da kuma hangen nesa - ƙaramin da mãsu haƙuri ne, da wuya ta myelofibrosis faruwa. A cikin m mataki da cutar, wanda zai iya ci gaba bayan 5-15, kuma ko da shekaru 20 bayan da ganewa na farko bayyanar cututtuka, da marasa lafiya na iya shẽƙe rikicin. Sa'an nan da cutar daukan kan siffofin da m cutar sankarar bargo: babban yawan hare-haren da ya bayyana a cikin gefe jini. Alamun wannan ci gaban a da cuta ne zazzabi, ãyõyin maye, m kuma hemorrhagic ciwo. An sau da yawa ya karu baƙin ciki , kuma hanta. A wasu marasa lafiya, yiwu m ci gaban da cutar tare da farkon bayyanar da ciwo na zub da jini da kuma haƙuri ta anemizatsiey.

The asibiti hoto subleukemic mieloza

Mafi sau da yawa marasa lafiya da damuwa bayyana janar wani rauni, wani nauyi a cikin ciki, wanda qara da motsi da kuma musamman ma bayan da abinci (shi ne saboda wani gagarumin karuwa a cikin baƙin ciki, kuma hanta). Akwai koke na ciwon kai, jin zafi a cikin kasusuwa da kuma kashin baya. Sosai da wuya, a cikin m mataki na cuta, da mãsu haƙuri iya ci gaba mai tsanani azanci shine disturbances. A likita dole ne dole ware myelosis funicular - a pathological yanayin juyayi tsarin da ya auku a lokacin da wasu megaloblastic anemia. Wannan yanayin sau da yawa yakan faru a cikin anemia, wanda ya auku a marasa lafiya tare da kasa ci na bitamin B12 a cikin jiki.

Bugu da ƙari kuma, sau da yawa faruwa thrombosis, wanda ya zama dalilin da ya karu yawan platelets a gefe jini a general, kuma krovi.Poslednee coagulation cuta iya lalacewa ta hanyar wani morphological rashin ci gaba ko da quite babban yawan platelets. Jima ko daga baya, thrombocytosis take kaiwa zuwa cin gaban splenomegaly, amma a cikin baƙin ciki fara rushe ba kawai platelets amma kuma cikin ja da maikacin jini, wanda ya haddasa ci gaban da anemia.

The nunawa shirin da kuma magani ga marasa lafiya zažužžukan

Ganewar asali "subleukemic myelosis" ya kamata a sa ba a kan tushen da na asibiti jini gwaje-gwaje, da kuma sakamakon da sternal huda ko iliac trepanobiopsy. Canje-canje a cikin jini gwajin ne sun fi mayar ba musamman da kuma kawai a kan katin shaida na karuwa ko raguwa a yawan jini Kwayoyin kuma canza su percentages ba za a iya bincikar lafiya "subleukemic myelosis".

Jiyya da cuta ne dogara da jihar na bargo da kuma samuwa kashi tsarin munanan. A wasu lokuta, isa tsauri kallo na haƙuri, alhãli kuwa da sauri ci gaba myelofibrosis ya zama alƙawari na jiyyar cutar sankara kwayoyi.

A cikin m mataki da cutar a wasu lokuta, bukatar sha radiation far, m nada jiyyar cutar sankara ga m myeloid cutar sankarar bargo magani shirin, kau na baƙin ciki - amma a cikin kowane hali da cutar magani da haƙuri kamata sanya wani m hematologist.

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