Kiwon lafiyaCututtuka da kuma Yanayi

Amniotic constriction: haddasawa, cututtuka, ganewar asali, da kuma magani regimen

Wani lokaci asibiti lafiya uwãyensu ba ta haifi jariran da morphological lahani: rashin phalanges, wata gabar jiki, har ma da shugabannin. The uwar yanke ƙauna, da ake zargi da kansa ko likitoci abin da ya faru da yaron. Wani lokacin da ta je fitina. Amma abin da gaske ne sabili da haihuwa lahani?

definition

Amniotic constriction, in ba haka ba da ake kira "amniotic kabu" ko "strands Simonara" wakiltar dublication amnion masana'anta wadda aka mĩƙe tsakanin igiyar ciki ganuwar. Kamar yadda mai mulkin, shi ba ya cutar da amfrayo da kuma ba ya gabatar da rikitarwa a lokacin haihuwa. Amma a rare lokuta, zai iya haifar da tsanani sakamakon.

Amniotic constriction - fiber filaments, wanda bayyana a cikin fetal mafitsara. Suna iya damfara ko bandeji da cibiyarki igiyar haɗe zuwa sassa na jiki na da tayin, haddasa haihuwa lahani (yanki na hannun, ƙafãfunmu, yatsun kafa, ko phalanges, wani lokacin decapitation).

dalilai

Akwai biyu theories me ya sa akwai amniotic constriction. A dalilan da wannan sabon abu bayyana m ruptures amniotic kumfa a farkon daukar ciki. Kamar yadda chorion ya rage m, da barazana da katsewa na tayi ci gaba ne ba a lura, amma thread cewa tashi saboda karya, free-iyo a cikin ruwar. Su za a iya guda biyu zuwa ga jiki na 'ya'yan itace. A cikin shakka daga ciki da jariri ke tsiro, amma thread kasance iri guda kamar yadda suka kasance, don haka akwai matsawa da nama ischemia kuma necrosis.

Wani lokaci daga baya, na biyu ka'idar, kamar yadda na farko bai gamsar shakka waɗanda lura cewa amniotic constriction (kirtani a cikin ciki na mace mai ciki) ya bayyana a lokaci guda tare da sauran nakasar malformations kamar kogon lebe ko cleft palate. Wadannan likitoci an nuna cewa, akwai makada saboda jijiyoyin bugun gini cuta ko cuta na fetal wurare dabam dabam.

Wani version of events ne intrauterine kamuwa da cuta, da kuma rauni a lokacin daukar ciki, mahaukaci genitalia (anya da ya zauna cikin mahaifa, biyu-horned mahaifa , da sauransu. D.), CIN (mahaifa gazawarsa), kumburi da amnion, endometritis, oligohydramnios. Amma babu wani daga wadannan theories An tabbatar a ƙarshe.

bincikowa da

A mafi yawan lokuta, asibiti da kuma awon ya kasa gane amniotic constriction. Hotuna daga duban dan tayi nazari uninformative, tun wadannan zaren ne bakin ciki sosai. Kaikaice ba za ka iya gane kara girman da kuma kumbura wata gabar jiki a wuraren matsawa. Sun fi mayar da tartsatsi overdiagnosis wannan Pathology. Saboda haka, idan wani likita ne da ake zargin gaban amniotic makada, ciki directed zuwa MRI da kuma 3D duban dan tayi.

Fiye da rabin kamu amniotic constrictions a maimaita duban dan tayi ba za a iya gano saboda su katsewa.

statistics

Dangane da fasaha kayan aiki prenatal mita tare da gano amniotic constrictions iya bambanta daga 1: 1200 zuwa 1:15 000 danginsu. An yi imani da cewa mutum ɗari biyu da dubu goma abortions faruwa ga wannan dalilin. Tamanin cikin dari na strands Simonara deform yatsun da hannãyenku, kuma wani goma bisa dari - a matsawa na cibiyarki igiyar. Wannan samuwar kullin a cibiyarki igiyar manyan zuwa hypoxia da antenatal fetal mutuwa.

Abin farin, mafi diagnoses "amniotic band constriction" ba da goyan bayan asibiti ko fibrous strands ba sa gagarumin cutar da tayin.

gadar hali

A yiwuwa cewa amniotic constrictions bayyana a lokacin daukar ciki, shi ne musamman kananan. Wannan ba wani hereditary cuta. Yawanci, da ilimin kwayoyin hali ko chromosomal maye gurbi faruwa symmetrically, kuma a cikin wannan yanayin, da thread a haɗe gaba daya bazuwar. Idan na farko ciki a cikin yaro strands Simonara lura, shi ba ya nufin cewa m yara za a ji rauni. Har ila yau, shi ba ya nufin cewa iyaye da suka sha wahala a utero amniotic band constriction, wani yaro da aka haife tare da malformations.

effects

Ko da yake amniotic constrictions - ba m Pathology, sakamakon shi ne sosai m. Saboda gaskiya cewa makada iya entangle fetal sassa na jiki, tasowa Lymph stagnation. Wannan take kaiwa zuwa edema da kuma necrosis. Bayan haihuwar irin wannan reshe dole ne, bisa, ko ci gaba murkushe-ciwo: da gubobi da cewa sun tara a cikin anesthetized reshe, fada cikin tsari dabam dabam da kuma gabobin za su fara kashe shi da guba baby. Wannan zai iya haifar da mutuwarsa. Saboda haka dole ka cire reshe, idan ta riga unsustainable. Kuma da sauri.

Bugu da kari, a cikin ciwo na amniotic constrictions iya depressions wata gabar jiki da kuma yatsunsu a cikin proximal ɓangare na reshe. M tsakanin wadannan yara kabu yatsun ko phalanges na yatsunsu da yatsun kafa. Wani lokaci, a Bugu da kari ga constrictions na yaro ne kiyaye sauran stigma disembriogeneza: kogon palate da babba lebe. A sosai rare lokuta akwai babban take hakki na kashin baya da kuma gyara man fuska kwanyar, eventration na ciki gabobin, atresia na cibiyarki igiyar.

Idan constriction rinjayar a hankali spaced receptacles ga fata, sa'an nan a wannan lokaci shi ne kafa hemangioma. Ƙari bayan haihuwa dole ne a cire.

Wasu masana kimiyya sami dangane igiyoyinsu Simonara tare da kwancen kafa. Wannan shi ne saboda fetal kafafu suna gyarawa fiber igiyoyin, don haka ya zauna cikin mahaifa iya damfara kafar da tayin. Ashirin bisa dari na wannan Pathology ne biyu-gefe. Wani hadarin, wanda ya samar da wani obstetrician - shi ne wanda bai kai ba haihuwa. Wannan wahala - a m sabon abu a ciki da cewa faruwa tare da ciwo amniotic constrictions.

magani

Matsayin mai mulkin, a utero yake akwai wata cuta ba za a iya warke. A likita yi, akwai anecdotal lokuta inda wani transvaginal ko laparoscopic tiyata. Amma shi ne wani matsananci gwargwado, kamar yadda pinched muhimmanci gabobin. Amma shi ne musamman rare amniotic constriction. Jiyya yawanci za'ayi bayan da a haifi jariri.

A zaruruwa suna dissected kuma, bisa wani ɓangare na wani reshe idan ya cancanta. Don inganta ingancin rayuwa za a iya transplanted yatsunsu saukar da makamai.

Outlook

A hangen nesa ga rayuwa da kuma kiwon lafiya, shi ne kullum m. Yara a mafi yawan lokuta girma da kuma ci gaba bisa ga shekaru. A kowace shekara da wata gabar jiki inganta, don haka asarar hannu da dantse, hannunka, ƙananan kafa ko kafar mai yiwuwa ne su tãyar da wani wucin gadi canza. Yara suna karfafa canza hakoran roba da kuwa sun tsufa. Idan constriction sa qananan aikin aibi, kwaskwarima lahani za a iya shafe ta da canja wurin yatsunsu da su phalanges.

A mutane da ciwo amniotic constrictions za a iya haife daidai da lafiya yara, kamar yadda wannan cuta ba a gaji.

Celebrities da suka yi makada Simonara

An yi wani lokaci a lokacin da mutane tare da reshe yanki da aka boye a gidajensu, da kuma ostracized da al'umma. Yanzu za su iya rayuwa tare da kusan babu hani, to rike muhimmanci jama'a matsayi, motsa jiki, ya bayyana a talabijin da kuma shiga cikin kyakkyawa gasar.

Wasu sanannun mutane ne ba na jin kunyar da aka haife tare nakasar yanki, amma ko da cewa shi ne saboda amniotic constriction - wani bude tambaya.

  1. Carrie Bornell - actress, wanda aka haifa ba tare da wata dama hannu da dantse. Yana aiki a kan yara talabijin tashar. Wannan ya sa a gauraye dauki a tsakanin matasa da masu kallo da kuma iyayensu, ya kuma ba impetus zuwa fitowan da jerin shirye-shirye game da yadda za a gaya wa yara game da tawaya, kuma musamman fasali na rayuwa daga wadannan mutane.
  2. Dzhim Ebbot ne saba wa duk magoya na baseball. Shi ne mai almara tulun, watau feed, ba tare da hakkin goga. Ya yi ritaya daga wasanni a karshen karni na ashirin, amma da misali ya ci gaba da wahayi zuwa gare su da yawa mutane da nakasa da kuma Paralympians.
  3. Teresa yukata - mai kyau Miss America, aka haifa ba tare da hagu. A lokacin gasa, ban sa wani prosthesis, ya nuna cewa ba za ka iya zama da kyau da kuma ba tare da wucin gadi sassa.
  4. Kelli Noks - saman model ba tare da wani hannu da dantse hagu. A shekarar 2008, ta lashe gaskiya show a kan BBC tashar 3. Bugu da kari mata a cikin wannan gasar da hannu bakwai 'yan mata da daban-daban nakasa.
  5. Nikolas Makkarti - mashahuri pianist, wanda aka haifa ba tare da wani hannun dama.
  6. Nikolas Vuychich - Australian Kirista wa'azi. Shahararren domin ana haife ba tare da wani wata gabar jiki. Ya wallafa littattafai da kuma ke zuwa taro a duk faɗin duniya a matsayin wani misali, ya kamata ka ba har ma a mafi wuya yanayi.
  7. Mark Goffeni - garaya, haife tare da gurguwar hannuwanku. Ya koya yi wasa tare da yatsun kafa.

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