Kiwon lafiyaMagani

Ataxia - menene wannan? Alamun da iri ataxia

Ataxia - shi ne ba tare da inna dysmotility, waxanda suke da halayyar fasali na kari cuta da kuma mota daidaituwa. Fassara daga Girkanci kalmar ataxia nufin "hargitsi" kuma "rikice".

Tare da wannan ganewar asali ƙungiyoyi zama disproportionate, m, m, sau da yawa shan wahala daga tafiya, kuma a wasu lokuta ma a jawabin. Ka yi la'akari da abin da iri ataxia tsaya da kuma abin da suke su halaye.

Friedreich ta ataxia

Friedreich ta ataxia - a genetically sa neurological cuta, wadda ake kira da a ci gaba da hali. A farko manifestations da cutar zama fili a cikin 'yan shekarun da farko na rayuwa.

Da farko, akwai take hakki na rubutun hannu da kuma Gait. Ga yara, duk da haka, bayyana wani take hakkin rubutun hannu ne da wuya saboda gaskiyar cewa ya ba tukuna cikakken kafa. Game da Gait, da mãsu haƙuri a cikin wannan hali yana bukatar goyon bayan, wanda ya kiyaye talking. All ƙungiyoyi na kafafu ne mafi jerky fiye da gudana.

Yana tasowa a kan lokaci rashin tsaya (astasia) da kuma ko tafiya (Abaza). Duk da haka, da karshen ne na hali bayyanuwar hanzari m Hakika na cutar da kuma ta karshe, saukarwa.

Ya lura canje-canje a cikin kashin baya, wanda yana da muhimmanci musamman ga matasa, a cikin abin da aiwatar da da samuwar ba a gama ba tukuna. A 'yan shekarun baya da haƙuri saboda kasawa a cikin aikin na pancreas ci gaba da ciwon sukari. A kadan daga baya saboda degenerative canje-canje a cikin gonads auku hypogonadism. A karshen matakai na ataxia shiga gani disturbances tasowa a sakamakon degenerative canje-canje a cikin na gani, kuma oculomotor jijiyoyi. A saman da cewa, saboda da lalata wa neurons a cikin kwakwalwa tasowa gigin-tsufa.

Da shan kashi na cerebellum

Cerebellar ataxia - wani rashin lafiya na mota daidaituwa, masu tasowa, tare da shan kashi na babban hali alhakin shi, jiki - kwakwalwa cerebellum. A wasu lokuta ɓullo da qananan canje-canje, da kuma a wasu - mafi tsanani da kuma nauyi.

A ci gaba da irin wannan ataxia auku view kẽwayẽwa yankuna daban-daban na cerebellum pathological tsari. Sau da yawa cerebellar ataxia kamu da encephalitis, cerebellar jijiyoyin bugun gini cututtuka, mahara sclerosis, m kwakwalwa marurai, guba, da kuma wasu cututtuka na kwayoyin asalin. Ware 2 iri cerebellar ataxia - a tsaye da kuma tsauri.

A tsaye yanayi na cerebellar ataxia

Cerebellar ataxia bayyana, a wani a tsaye view of akan rage tsoka sautin. A haƙuri a kan aiwatar da shi ya zama da wuya ga wani dogon lokaci zauna a wuri guda, kamar yadda ya kasance qananan take hakki na mota daidaituwa. Man motsa sosai m da staggering matakai kamar shi ne a Jihar maye. A tsanani lokuta, da haƙuri da cutar ba zai iya zama da tsaya, saboda, ba da ciwon da ƙarfi ko da rike kansa, ya aka kullum fadowa. A tsaye ataxia a mai tsanani deprives haƙuri da ikon ci gaba da sikẽli a kan nasu. Shi ne ya kamata a lura da cewa a motor daidaituwa ba ya shafar abin da yake a haƙuri da bude ko rufe idanu.

A tsauri yanayin cerebellar ataxia

Amyotaxy ɓullo da tare da hannu na cerebellar hemispheres a pathological tsari. Idan iri-iri da cutar Coordination cuta ne kiyaye kawai a lokacin da jiki motsi. Rasa santsi da kuma daidai ƙungiyoyi, suna shara da kuma m. Discoordination da slowing na ƙungiyoyi lura a shafa gefe. Domin tsauri ataxia ne halin hypermetric (wuce kima, tsaurin zirga-zirga) adiadohokinez, promahivanie da niyyar tsãwa da kuma jawabin cuta (marasa lafiya Talk ragae ta watse kalmomi a cikin syllables).

A tsaye da kuma tafiya haƙuri ne deflected a cikin m lalace cerebellar yammancin duniya gefe. Canjãwa haƙuri da rubutun hannu: shi ya zama m, m, manyan haruffa. Yana yiwuwa rage agara reflexes.

azanci shine ataxia

Wannan ataxia - wani rashin lafiya na motsi, a cikin abin da wani canji na Gait auku saboda asarar abin mamaki a kafafu, wanda shi ne wani sakamako na gefe jijiyoyi, da tsakiya madauki, raya ginshiƙai da na baya tushen da laka. A haƙuri ba ji da matsayi na kafafu, da kuma saboda haka yana da wahala duka biyu lokacin da tafiya da kuma lokacin da a tsaye. Matsayin mai mulkin, ya aka tsaye da kafafu da fadi da baya da kuma a lokaci guda zai iya ci gaba da auna kawai tare da idanu bude ba, amma idan suka rufe, sa'an nan da mutum ya fara yawo da yake iya fada (m alama na Romberg). Lokacin da tafiya, da marasa lafiya ma straddle kuma ya dauke su ya fi yadda ya cancanta, da kuma impulsively talking shi baya da kuma fitar. Su matakai ne na daban-daban tsawo, da kuma kafar da taba da kasa, buga snapping sautuna. A haƙuri ne tafiya kullum yana amfani da wani itace ga goyon baya da kuma 'yan bends a cikin hip gidajen abinci jiki. Gait tsangwama tsananta gani lahani. marasa lafiya sau da yawa rasa su da kwanciyar hankali, lilo da kuma fada a lokacin da wanke fuskarka, kamar yadda ya rufe idanunsa, suka rasa lokaci na gani iko.

spinocerebellar ataxia

Wannan kalma tana nufin wani jam'i na mota cuta tasowa mafi yawa saboda ischemic CNS rauni ko perinatal hypoxia. Tsanani canje-canje a Gait iya zama daban-daban da kuma dogara a kan mai tsanani da kuma yanayi na rauni. Kamar wancan ne, haske zai iya sa rauni iyaka Babinski, ta ƙara agara reflexes, kuma ba tare da wani alama a canza a Gait. M, kuma mafi tsanani raunuka yawanci ya kunsa gefe hemiparesis. Canje-canje faruwa da key Gait halayyar paraparesis.

Cerebral palsy haifar motsi cuta ya kunsa canje-canje a Gait. Marasa lafiya haka akwai involuntary ƙungiyoyi daga cikin wata gabar jiki, wanda suna tare da grimaces a kan fuska ko wuyansa juyawa ƙungiyoyi. Matsayin mai mulkin, kafafu mika da makamai lankwasa, amma wannan reshe jeri na bangaren iya zama na fili ne kawai bayan da wani m kallo na haƙuri. Alal misali, daya hannu za a iya kara da a juye zuwa kasa da kuma sauran supinated da flexed. A asymmetric matsayi na wata gabar jiki da kuma sau da yawa faruwa a lokacin juya your shugaban a daban-daban kwatance.

ganewar asali ataxia

Domin ganewar asali ta amfani da bincike dabaru irin su:

  • MRI na kwakwalwa.
  • kwakwalwa electroencephalography.
  • DNA bincikowa.
  • electromyography.

Bugu da kari ga wani daga cikin da aka ambata hanyoyin wajibi ne a dauki wani jini gwajin, za a yi nazari da kwararru kamar wani neurologist, likita hauka da ophthalmologist.

ataxia magani

Ataxia - mai tsanani cutar da bukatar dace mataki. Jiyya wanda zai gudanar da gwani neurologist, zai fi dacewa shi ne symptomatic da ya hada da wadannan yankunan.

  1. Restorative far (anticholinesterases, "Cere" ATP, B bitamin).
  2. Jiki far da nufin hana daban-daban iri rikitarwa (atrophy kuma murdede contractures, misali) inganta tafiya da kuma co-keɓewa,, rike motsa jiki da jini.

Musamman dakin motsa jiki hadaddun motsa jiki motsa jiki far, manufar wanda shi ne don rage incoordination da kuma karfafa tsokoki. Lokacin da wani m magani Hanyar (tiyata cerebellar marurai, misali) za a iya sa ran wani m ko cikakken maida ko akalla daina kara ci gaban.

A Friedreich ta ataxia, shan la'akari da pathogenesis da cutar, za su iya taka wata babbar rawar kwayoyi da nufin rike mitochondrial aiki ( "riboflavin", bitamin E, coenzyme Q10, succinic acid).

A hangen nesa da cutar

Hasashen na hereditary cututtuka ne quite ya fi karfinsu. A tsawon lokaci, musamman idan yana da rago, neuropsychiatric cuta kawai ci gaba. Mutane da ganewar asali "ataxia", da bayyanar cututtuka na wanda da shekaru zama mafi pronounced, kamar yadda mai mulkin, ƙwarai rage ikon aiki.

Duk da haka, saboda symptomatic magani, kazalika da rigakafin maye, da kuma raunin da cututtuka, marasa lafiya rayuwa ga tsufa.

rigakafin

Don dauki m matakan musamman domin ataxia ba zai yiwu ba. Da farko, shi ne ake bukata don hana yiwu fitowan da kuma ci gaban mai tsanani cutar (sinusitis, otitis, ciwon huhu, misali) na iya sa ataxia.

Wajibi ne a kauce wa jini aure. Bugu da kari, ya kamata a tuna da cewa yiwuwar samun yaduwar hereditary ataxia daga iyaye zuwa yaro, kuma domin da marasa lafiya sukan rika dakatar da haihuwa na da nasu 'ya'yan, kuma ya dauko wani ta yaro.

Ataxia - mai tsanani neurological cuta, to abin da za ka so ka fara nan da nan magani. Shi ya sa da jima da wannan cuta da aka gano, da mafi alhẽri ga mãsu haƙuri da za a yi hasashen.

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