Caroli ta cuta: Bayyanar cututtuka da kuma Jiyya

Caroli ta cuta ne mai matukar hadaddun aikin tashin hankali na hanta, bincike da kuma magance wanda ya haddasa tsanani ga likitoci.

Abin da yake akwai wata cuta

Caroli Cuta - rare nakasar da hanta da cutar lalacewa ta hanyar fadada daga cikin bile ducts, located cikin jiki. An halin a cewa da al'ada da zirga-zirga da aka lalace bile stagnation ya auku da kuma ta Accession kamuwa da cuta. Sau da yawa da cuta ne na kowa a maza, kuma shi ya fara tare da yara, ko kuma samartaka. A ci gaba da pathological tsari ya dogara da adadin da mataki na lalacewar da ducts cikin hanta.

siffofin da cutar

Don kwanan wata, wani m rarrabuwa na Caroli ta cuta a cikin magani aka bata. Duk da haka, duk da wannan, akwai biyu daban-daban siffofin da cutar. A farko nau'i ne halin a cewa karye biliary patency, tare da m samuwar duwatsu.

Na biyu form dangantawa da nakasar hanta fibrosis. A wannan yanayin, akwai wani kadan fadada daga cikin ducts da kuma samuwar duwatsu ne zai yiwu, ko da yake mai yiwuwa wasu lokuta faruwa a baya, saukarwa da cutar.

Advanced bile ducts iya haɗa zuwa yankunan da cystic hanta da haka visualized bangare bango thickening a mafitsara lumen.

Sanadin

Caroli cuta tana nufin wani nakasar cututtuka tasowa saboda wani autosomal recessive yanayin na gādo. Idan kana da mafi kusantar dangi da irin wannan Pathology, bayan haihuwar yaro nan da nan bukatar gudanar da wani m jarrabawa, kamar yadda akwai wani mafi girma da damar wucewa a kan hereditary cututtuka.

A wasu lokuta, da cutar da ake kuma shiga da sauran pathological cuta na hanta, wadda ƙwarai dagula magani.

Babban bayyanar cututtuka

Caroli ta cutar bayyanar cututtuka zai iya bayyana kansu a cikin gaba daya kowane zamani a yara da kuma matasa. Yana yiwuwa a gudanar da wani babban fasali na cuta, kamar:

• ciki zafi.
• zazzabi.
• kadan yellowness da fata.
• hanta kara girma a kan palpation.

Alamtacce a asibiti manifestations da cutar sukan hade tare da ya faru na kumburi. M Caroli cutar da ake bincikar lafiya a namiji yara. A wani exacerbation ya kasance mai kaifi karuwa a matakin na bilirubin da fari jini cell count.

Aikin ne

Duk da cewa da bayyanar cututtuka da cutar isasshe bayyana, amma shi ne ma halayyar wasu hanta cuta. M ganewar asali da kuma sanin ko zai yiwu Caroli ta cuta a cikin Amurka da kuma a lokacin CT. Lissafta tomography an dauki daya daga cikin mafi m hanyoyin da jarrabawa, saboda ba za ka iya ganin ta isa dukkan keta dokokin. Bugu da kari, endoscopic cholangiography iya da ake bukata domin ganewar asali.

Hanta aiki gwaje-gwaje na dogon lokaci ba ya canza, duk da haka, tare da ci gaban da cutar da kuma shafe tsawon kumburi tsari a cikin biochemical bincike na jini iya gane duk da ãyõyin cholestasis.

Saboda marasa lafiya ne a hadarin cholangiocarcinoma, Bugu da kari ya kamata a za'ayi da serological nunawa ga gaban ƙari saka alama.

Features na magani

A gaban Caroli cuta magani jagororin dole a lura ba tare da kasa ba, domin wannan Pathology ne m, a yanayi. Jiyya nufin da aikace-aikace na m-bakan maganin rigakafi, da kuma ursodeoxycholic acid gwamnati matsayi hana ilimin lissafi samuwar.

Bugu da kari, da magani qunshi:

• analgesics.
• litholysis duwatsu.
• biliary magudanun ruwa.

Bayan Accession, cholangitis, ko wasu rikitarwa na surkin jini far ne ba daban-daban daga jiyya na kwayan cholangitis. Yana da muhimmanci a cire ruɓaɓɓen jini, sa'an nan tsarkakewa ne da za'ayi na bile bututu, da kuma amfani da maganin rigakafi don taimakawa wajen cire kamuwa da cuta.

The aiki aka yi kawai a yanayin saukan m exacerbations ko m amfani da ra'ayin mazan jiya dabaru. A girma daga m baki na iya bambanta da yawa. kawai duwatsu ko biliary sassa za a iya cire shi ba.

A cikin hali na da karfi fadada wurare da kuma biliary bile stagnation, Likita zai gudanar da kau da daya lobe daga cikin hanta. A tsanani lokuta, hanta insufficiency a gaban ko alamun degeneration a cikin m ƙari, wata hanta dashi iya bada shawarar daga makusancin zumunta ne.

Don kyakkyawan sakamako, mafi likitoci bada shawara jawabin da wasu hanta dasawa ko in babu mai tsanani bayyanar cututtuka a matakin farko na cutar. Sau da yawa, duk da haka, gaban kamuwa da cuta ne contraindication zuwa dasawa. marasa lafiya rayuwa kudi bayan dasawa da nakasar fibrosis cewa an bugu da žari kamu cholangitis a lokacin dasawa, shi ne wajen low.

Hangen nesa da wannan cuta quite fi karfinsu, tun dakwai, komowan cutar na iya faruwa a shekaru da dama. Duk da haka, da wuya sosai shi results a cikin mutuwa daga mãsu haƙuri.

Caroli cuta

Caroli Cuta quite sau da yawa dangantaka da nakasar hanta fibrosis, sakamakon wani Caroli cuta. Duka wadannan pathologies an kafa ta kusan m form biliary cuta a cikin hanta nama a matakin tayi ci gaba. A ciwo da aka gada a kusa zumunta da bayyana ciki zafi da kuma zub da jini daga esophageal varices. Neonates iya zama a hade da babban bayyanar cututtuka na nakasar hanta fibrosis, Caroli cutar da kuma polycystic koda cuta.

Wannan cuta tana nufin wani nakasar bile bututu mafitsara, duk da haka, shi ne quite rare, kuma mafi yawa a cikin mutane masu shekaru a karkashin shekaru 30. A farko 'yan shekaru na Pathology auku kusan asymptomatic, muddin fadada daga cikin bile ducts kada ku sa stagnation na bile, wanda zai haifar da yanayi na samuwar duwatsu da Accession kamuwa da cuta. Idan amfani tare da sauran lura ãyõyin jaundice, shi ya nuna gaban cholangitis.

Yana bikin yafi hagu-gefe hanta lalacewa, amma kuma yana iya zama wani biyu-hanya a wasu lokuta.

A wasu lokuta, da hanta ne da karfi da cewa zai iya shafar sauran gabobin. Saboda haka daya daga cikin matsalolin da za a iya gani, kamar yadda ya faru na koda gazawar.