Kiwon lafiyaCututtuka da kuma Yanayi

Hemolytic-uremic ciwo - abin da yake da shi?

Hemolytic uremic ciwo ne wani alama, wanda aka bayyana a cikin nau'i na hemolytic anemia, OPN da thrombocytopenia. A karo na farko da wannan cuta da aka bayyana a cikin shekara ta 1955. A cewar masana, game da 70% na lokuta da ganewar asali a cikin yara na shekarar farko ta rayuwa, da kuma kawai 'yan faru rubuce a cikin manya. A wannan labarin, za mu magana game da wannan cuta, da kuma dubi yadda za a bi da da hanyoyin zamani na hemolytic uremic ciwo.

nan da nan haddasawa

A ci gaba da wannan cuta kwararru a yanzu ake dangantawa da dalilai da dama. Da farko wannan kwayar kai tsaye mai guba lalacewar capillary endothelium don haka ya kira glomeruli. A daya hannun dalilin iya karya a cikin DIC kuma inji lalacewar erythrocytes. An yi imani da cewa karshen za a iya lalace a lokacin nassi ta hanyar capillaries na glomeruli kansu, abin da suke a nuna cika da fibrin clots.

babban bayyanar cututtuka

Hemolytic-uremic ciwo faruwa yawanci a yara da m karu a fitsari fitarwa, amma in babu shakka akwai ayoyi na dehydration da kuma a kan bango na gwada al'ada VEO sigogi. Idan wani jariri yana da wani zazzabi ko amai ya bayyana fi yiwuwa cutar progresses hanzari - akwai wani cerebral edema. Sau da yawa, hemolytic uremic ciwo ne complemented kodadde-skinned yaro, a rare lokuta, da kananan eruptions.

diagnosing

Don tabbatar da irin wannan ganewar asali a matsayin hemolytic-uremic ciwo, dole ne ka wuce jerin gwaje-gwaje, ciki har da cikakken jini analysis. Kawai bayan cikakken jarrabawa na haƙuri iya magana game da kara magani.

Hanyoyin zamani na magani

More kwanan nan ba da lifiya mace-mace da aka sosai high (80 zuwa 100%). Duk da haka, masana kimiyya suna kullum neman warware wannan matsala. Kuma haka dai aka halitta da na'urorin da ake kira "wucin gadi koda", godiya ga wanda lamarin ya canja matu. Yau, mutuwar kusan taba faruwa (tsakanin biyu da kuma goma bisa dari). Suna iya zama kawai a lokacin marigayi cutar ganewa, kazalika da a ci gaba da komowar matakai a cikin kwakwalwa saboda da kumburi. Ya kamata a lura da cewa irin wannan ganewar asali ne atypical hemolytic uremic ciwo, kullum bukatar daga 2 zuwa 9 zaman (yau da kullum) ta amfani da "wucin gadi koda". By wannan dialysis kwararru iya kula da al'ada matakan metabolites, kazalika da hana kwakwalwa kumburi.

Outlook

Hanyoyin zamani da damar da yara mu jimre wa wannan matsala. Duk da haka, wannan mai yiwuwa ne kawai a cikin taron cewa rashin lafiya da aka gano a cikin farkon, saukarwa. In ba haka ba, da alama na da cikakken warke da ɗan ƙananan. A cewar masana, da halin da ake ciki a cikin rashi na wani m mayar da martani a kan sashi na jiki bayan 2-3 zaman na hemodialysis, tsinkaya sosai ya fi karfinsu.

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