Dubin-Johnson ciwo: description, ganewar asali, cututtuka da kuma magani

Duk da cewa zamani magani ya sanya babban ci gaba da yawa cututtuka ne ba da jumla ga marasa lafiya, wasu daga wadannan cututtuka ne ba tukuna cikakken gane. Daya daga cikinsu shi ne dubin-Johnson ciwo. A asibitin da bincike da kuma lura da wannan cuta babban ga kiwon lafiya kwararru na wasu amfani. Ka yi la'akari da wannan tambaya a cikin mafi daki-daki.

Na'ura mai juyi ciwo da dubin-Johnson ciwo - a rare hereditary cutar hanta Similar juna jaundice.

Sanadin

Dubin-Johnson ciwo ma yana da wani sunan: enzimopaticheskaya jaundice hanta. Yana taso dangane da take hakkin da ceto a cikin bile daga hanta sel bilirubin.

Wannan abu bayyana a cikin jiki domin kau gare lalace ko gaba daya hallaka erythrocytes. Kammalawa bilirubin faruwa a hanyoyi biyu:

• kara adadin abu da yake fita ta cikin bile.
• adadi kaɗan na fitsari je.

Dubin-Johnson ciwo ya auku a lokacin da disrupted kai na bilirubin via da bile. Wannan sigar musamman rare cuta mai saukin kamuwa zuwa mafi samari (game da 20-30 shekaru). lokuta da cutar tun haihuwa wani lokacin faruwa. A hadarin kamuwa da cuta bayan da shekaru mutum 50 shekara ko dadadde ne kadan.

A kayyade hanyar da ciwo, dubin-Johnson ne saboda wani gene maye gurbi, tafiyar da fitarwa na bilirubin a cikin hanta da kuma shigar da sunadarai.

cututtuka

Dubin-Johnson ciwo, cututtuka daga waxanda suke da halayyar da wasu cututtuka irin su, misali, gajiya, kuma yana da bayãnin hukuncin fasali:

• zafi a cikin hakarkarinsa a gefen dama.
• cikakken rashin ci.
• akwai iya zama kadan itching na fata;
• kara girman hanta.
• colic, wanda wani lokacin qara.
• amai.
• da yawan zafin jiki karuwa.

Bayyananen ake Littafi saboda cututtuka, mai tsanani jiki da kuma wani tunanin obalodi. Ga mata, zai yiwu ƙarin tsanani bayan ci na hana.

hadarin kungiyar

Wanne rukuni na mutane ya zama wary na ciwo?

A cuta ne hereditary. Idan iyali da 'ya'ya tare da wannan cuta, da biyu a mataki na shiryawa da ciki wajibi ne a wuce duk gwaje-gwaje, wuce da zama dole gwaje-gwaje da kuma tuntubar da gwani. Wadanda shawarwari ne dacewa ga wadanda ma'aurata, ciki har da daya daga cikin maza ko su kusantar dangi suka sha wahala dubin-Johnson ciwo.

The bincike tsari

Geographically, cutar ne ya fi kowa tsakanin Iran Yahudawa. Adadin su ya kai 70% na jimlar nauyin da waxannan cututtukan marasa lafiya.

Yana da muhimmanci cewa kusan babu rayuwa-barazanar dubin-Johnson ciwo. MISALI marasa lafiya tabbatar da wannan. Doctors yayi nazari da rayuwa Hasashen na marasa lafiya da wannan cuta da kuma ƙarasa da cewa shi ba ya kai ga mutuwa.

Game da 25% na marasa lafiya sun dandana shan azaba a hannun dama hypochondrium. A tsarin da hanta ba ya canzawa, to, bãbu nakasawa a cikin ciwo. Amma a lokaci guda a cikin kyallen takarda bayyana black spots, sakamakon shi a jiki ta sauya launi zuwa kore ko duhu launin ruwan kasa. Wannan yanayin na ciwo ne ake kira cakulan guntu cookies. Wannan sakamako ne cimma wani warwarewarsu metabolites mugunya.

A cuta yana da wani m hangen nesa, ko da yake da shi zai iya ci gaba da cikin rayuwar haƙuri.

Tebur a kasa nuna bayanai a kan matsayi na ciki gabobin da marasa lafiya.

bincikowa da

Dubin-Johnson ciwo, da ganewar asali wanda faruwa a dama, saukarwa, m da ƙididdiga.

• Shi ne m zuwa duban dan tayi na ciki.
• Janar jini da fitsari gwaje-gwaje.
• Analysis na jini da kuma fitsari ga bilirubin. Matsayin mai mulkin, su ne ma high.
• Samfurori fenobarbetalom.
• Alamomi na hepatitis.
• Samfurin bromsulfaleinova.
• Coproporphyrin darajar Manuniya a cikin fitsari a kowace rana.
• Da abun ciki na enzymes a cikin jini.

Aiwatar da wasu sauran hanyoyin da ganewar asali.

A gaban dubin-Johnson ciwo marasa lafiya da ya ziyarci wani ilimin.

Magani da kuma rigakafin

Dubin-Johnson ciwo, wanda magani ba ya unsa samun shirye na musamman sarrafawa da m matakan:

• riko da wani m rage cin abinci, da yin amfani da B bitamin, wadanda ba preservatives.
• raguwa a danniya yanayi.
• akan rage jiki aiki.
• sãma da giya.
• Regular saka idanu na bilirubin matakan a kan rayuwa na haƙuri ta rayuwa.

Shi ne kuma dole a tuna cewa ciki na iya exacerbate cutar. Kwayoyi don taimaka warkar da ciwo dubin-Johnson, a halin yanzu ba ci gaba.

Hakazalika, yanayin da cuta ne na'ura mai juyi ciwo.

taƙaitaccen bayanin

Na'ura mai juyi ciwo kuma shi ne mai hereditary cutar da ke shafar cikin hanta. Shigarsu canje-canje a cikin bayarwa na bilirubin, enzyme ayyuka zama al'ada. Za mu iya cewa da cutar ne a hur nau'i na dubin-Johnson ciwo aka bayyana a sama. Alamun kuma bayyana kadan softer.

Cutar na iya bayyana a matsayin daga haihuwa da kuma yaranta. Bilirubin a cikin jini na haƙuri iya zama free kuma mamaye. Akwai bambanci na gallbladder.

Na'ura mai juyi ciwo ne halin da cewa a hepatocytes babu abun ciki na ruwan kasa pigments. Ba akwai wani sakamako, wanda aka sani da cakulan guntu cookies. A sabili da cutar ne dan kadan daban-daban daga dubin-Johnson ciwo. A wannan yanayin, da hanta ba zai iya jimre da sha na bilirubin. A sakamakon haka, gazawar undigested abu da baya a cikin jini. A wannan hasashe, a cikin haƙuri tasowa giperbulemiya. M hangen nesa da cutar.

A lokacin da lifiya lidofreninom hanta, gall mafitsara da kuma ducts ne bayyane.

ciwo cututtuka

ÃyõyinSa na'ura mai juyi ciwo ne sosai kama da bayyanar cututtuka na ciwo dubin-Johnson:

• Jabu bayyana jaundice.
• The ji na haushi a cikin bakinsa.
• Pain a dama hypochondrium.
• Lokacin da dubin-Johnson ciwo, hanta marasa lafiya ya karu a size. A cikin hali na na'ura mai juyi ciwo ne ta ƙara kawai a wasu lokuta.
• Dagagge matakan bilirubin a cikin jini.
• hanta aiki gwaje-gwaje ne na al'ada.
• jini gwaje-gwaje ba tare da canje-canje.
• A hanta bioptome ne babu jari na pigments.

Hangen nesa kullum m, da ciwo ya auku a kan shekaru masu yawa, ba ma compromising mutum kiwon lafiya.

ganewar asali na ciwo

Cutar za a iya kafa a lokacin da wani m ganewar asali da kwayoyin.

Nazarin gudanar a dakin gwaje-gwaje don taimaka bayyana wani karin abun ciki na bilirubin a cikin jini. Ga ganewar asali yana da muhimmanci a san yawan coproporphyrin dauke a cikin fitsari.

A mafi yawan marasa lafiya, cutar progresses ba tare da wani bayyanar cututtuka.

A cikin hali na ganewar asali na na'ura mai juyi ciwo ciyar hanta jarrabawa: ta X-ray, kuma duban dan tayi. A cikin wannan bincike sha gall mafitsara da kuma ducts.

cutar rigakafin

Janar m matakan kamar haka:

• akan rage jiki aiki.
• magani na cututtuka hade na'ura mai juyi ciwo.
• Guje wa danniya da kuma wani tunanin danniya.

Dalilai na karuwa bilirubin a cikin jini

Bilirubin ƙaruwa ga wadannan dalilai:

• tsananin gajiya.
• m rage cin abinci, da rage cin abinci take hakkin.
• da amfani da kwayoyi.
• wuce kima yin amfani da barasa.

magani na cutar

Common hanyoyin kawar da cutar a can. Duk da haka, dole ne bi da m matakan. Kamar yadda kwayoyi buƙatar ka kai yana nufin cewa fitarwa bilirubin daga jiki. Bile ne sau da yawa kwayoyi suna amfani.

Zabi da ya dace magani don taimaka likita.