Kiwon lafiyaCututtuka da kuma Yanayi

Myeloproliferative cuta: haddasawa, cututtuka, da lifiya

Myeloproliferative cuta haddasawa, cututtuka, ganewar asali wanda za a tattauna daga baya, qumshi da wani rukuni na jihohi, da abin da bargo, a can ne ta ƙara samar da thrombocytes, erythrocytes ko leukocytes. A total akwai shida daban na pathologies.

Overview

Bargo kullum aikin tsara kara (m) Kwayoyin. Bayan wani lokaci suka girma, zama cikakken. A kara cell iya zama masomin da samuwar iri biyu abubuwa: a yawan lymphoid da myeloid Kwayoyin. M Kwayoyin suna da hotuna da samuwar leukocytes. Daga cikin abubuwa na myeloid jerin suna samar:

  • Erythrocytes. Sun kawo oxygen da kuma sauran gina jiki sadarwa zuwa gabobin da kyallen takarda.
  • Leukocytes. Wadannan abubuwa ne da alhakin 'yan adawa da kuma sauran cututtuka pathologies.
  • Platelets. Wadannan Kwayoyin hana zub da jini, nau'i clots.

Kafin canji a cikin ja da maikacin jini, da farin jini Kwayoyin ko platelets, kara Kwayoyin bukatar tafi, ta hanyar da dama, saukarwa. Idan ba, myeloproliferative cuta, babban adadin fara abu ne kafa ta daya ko fiye iri kafa Kwayoyin. Yawanci Pathology progresses sannu a hankali isa tare da kara da wuce haddi jini abubuwa.

rarrabuwa

Type wanda zai iya samun myeloproliferative cuta ya dogara da adadin erythrocytes, platelets ko leukocytes. A wasu lokuta, jiki ne alama wuce haddi na abubuwa na fiye da daya jinsin. Pathology ne zuwa kashi:

  • Kullum neutrophilic cutar sankarar bargo.
  • Polycythemia.
  • Kullum myelogenous cutar sankarar bargo.
  • Essential thrombocytopenia.
  • Idiopathic (na kullum) myelofibrosis.
  • Eosinophilic cutar sankarar bargo.

pathological mataki

Kullum myeloproliferative cutar za a iya canza kama zuwa m cutar sankarar bargo. Wannan yanayin ne halin da wani wuce haddi na farin jini Kwayoyin. Kullum myeloproliferative cuta yana da wani takamaiman staging makirci. Warkewa matakan dogara ne a kan irin Pathology. Game da tafarkin da, da myeloproliferative cuta na iya faruwa a daya daga hanyoyi uku:

  • Germination a wasu kyallen takarda. A wannan yanayin, da ciwon daji bazuwa zuwa da kewaye lafiya segments, bugawa su.
  • Lymphogenous hanya. Myeloproliferative cuta iya shiga cikin lymphatic tsarin da receptacles rarraba a kan sauran tsokoki da kuma gabobin.
  • Hematogenous hanya. Sel malignancy shiga cikin capillaries da kuma jijiyoyinmu da cewa ciyar da kyallen takarda da kuma gabobin.

Lokacin da wani yaduwar ciwon daji Kwayoyin, mai yiwuwa kafa sabuwar (secondary) maruran. Wannan tsari shine ake kira metastasis. Secondary da primary marurai, suna wannan irin ciwon daji. Alal misali, akwai wani yaduwar leukemic Kwayoyin a cikin kwakwalwa. Yana sami ƙari abubuwa. Su koma ga cutar sankarar bargo, ba kwakwalwa ciwon daji.

ãyõyin Pathology

Ta yaya myeloproliferative cuta? Alamun da wadannan cututtuka:

  • nauyi asara, anorexia.
  • Gajiya.
  • Ciki da rashin jin daɗi da kuma abin nufi da azumi abinci jikewa. Last tsokani kara girman baƙin ciki (splentomegaliey).
  • Predisposition zuwa jini, bruising, ko bayyanar cututtuka na thrombosis.
  • Illa sani.
  • Hadin gwiwa zafi, kumburi, tsokani gouty amosanin gabbai.
  • Ringing a cikin kunnuwa.
  • Soreness a hagu na sama quadrant na ciki da kuma hagu kafada, wanda shi ne wani sakamako na kumburi ko infarction na baƙin ciki.

duba

Myeloproliferative jini cuta da aka gano a kan tushen da dakin gwaje-gwaje sakamakon. A binciken da ya hada da wadannan ayyukan:

  • Jarrabawa na haƙuri. A wannan yanayin, da gwani kayyade janar yanayin nuna alamun Pathology (busa, misali), kazalika da nuni, babu lafiya mutumin. Likita ya kuma gaya game da haƙuri da salon, cututtuka da kuma miyagun halaye, rubũta.
  • Fadada KLA. Jini daukan samfur ne da za'ayi domin sanin:

    - yawan platelets da kuma ja da maikacin jini.
    - rabo da yawan leukocytes.
    - matakin haemoglobin.
    - ƙara da wanda aka shagaltar da ja jini Kwayoyin.
  • Tsammãni, kuma bargo biopsy. A lokacin hanya, wani lokacin farin ciki da m allura da aka gabatar a cikin sternum ko iliac kashi. Wannan magudi ba ka damar daukar wani bargo samfurin da kuma nama, kazalika da jini. The abu ne yayi nazari a karkashin wani microscope for gaban mahaukaci Kwayoyin a cikinsa.
  • Cytogenetic analysis. Wannan hanya ba ka damar gane canje-canje a cikin chromosomes.

Kullum myeloproliferative cuta: Jiyya

Don kwanan wata, akwai da dama cuta hanyoyin kwantar da hankali. Daya ko wasu zaɓi an zaba dangane da yanayin haƙuri, kuma bayyananen cewa bi myeloproliferative cuta. A lura za a iya gudanar da misali - tabbatar yi, ko gwaji. Zabi na biyu shi ne don nazarin yin amfani da daban-daban sabon wajen.

phlebotomy

Wannan hanya yana shan jini daga jannayẽnsa. The abu ne sai ya aika wa kowa biochemical analysis. A wasu lokuta, phlebotomy wajabta wa marasa lafiya da suke kamu da myeloproliferative cuta. Jiyya a cikin wannan harka nufi ga rage yawan erythrocytes.

platelet apheresis

Wannan hanya ne kama da baya daya. Bambanci ne cewa babu ne da za'ayi da kau da karin platelets amfani da musamman kayan aiki. A haƙuri daukan cikin jinin da aka ratsa SEPARATOR. Ya riqe platelets. "Tsarkake" jini baya ga mãsu haƙuri.

transfussion

Wannan hanya ita ce mai jini. A wannan yanayin da aka canza wasu sauran abubuwa. A musamman, da mãsu haƙuri maimakon su halakar da kuma lalace Kwayoyin samun wani transfussion na fari da maikacin jini, ja jini Kwayoyin da platelets.

jiyyar cutar sankara

Wannan hanya da ya shafi yin amfani da cytotoxic kwayoyi. Su mataki ne da nufin rushe na ƙari Kwayoyin ko slowing da girma da siffofin maruran. Domin baka, igiyar jini ko intramuscular aikace-aikace na kwayoyi, da aiki sinadaran shiga cikin tsari wurare dabam dabam, kawar pathological abubuwa. Wannan ake kira tsari jiyyar cutar sankara. Regional dabara ne wani gabatarwar yana nufin a cikin kashin baya canal, da shafa sashin jiki ko jiki rami kai tsaye.

radiation far

Jiyya ne da za'ayi amfani da wani high mita x-ray ko wasu radiation. Radiation far iya cimma cikakken kawar da ƙari Kwayoyin da kuma rage da girma da siffofin maruran. A yi, a iri biyu magani. External radiation far ne da daukan hotuna na naúra, located gaba ga mãsu haƙuri. Lokacin da wani ciki cika tsari ne da za'ayi ta rediyoaktif abubuwa needles, catheters, shambura, wanda aka sa'an nan allura kai tsaye a cikin ƙari ko a cikin kyallen takarda located a kusa da shi. Wanne Hanyar Za a yi amfani gwani, dangane da mataki na malignancy na tsari. Marasa lafiya da suke kamu da myeloproliferative jini cuta ne irradiated, kamar yadda mai mulkin, da baƙin ciki yankin.

Jiyyar cutar sankara da dasawa na sel

Wannan Hanyar magani ne aikace-aikace na kwayoyi a high allurai da kuma canzawa shafi antitumor mataki na sabon Kwayoyin. M abubuwa ne daga wani mai bayarwa ko haƙuri kuma daskararre. Bayan kammala jiyyar cutar sankara, da aka gabatar a cikin jiki da kayan adana. Innovations Kwayoyin fara girma da kuma ta da da samuwar sabuwar jini Kwayoyin.

dawo da lokaci

Bayan da magani, da mãsu haƙuri kamata ganin likita a kai a kai. Don kimanta tasiri na far iya da ake bukata don gudanar da wani jerin hanyoyin amfani a baya kafin saduwa. A daidai da sakamakon, yanke shawara a kan ci gaba, ƙarshe ko canji na lura regimen. Wasu safiyo ya kamata a maimaita a ranar akai-akai, ko da bayan kammala warkewa hanya. Su ka damar tantance tasirin abubuwan da gane wanna sake komowa.

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