Kiwon lafiyaCututtuka da kuma Yanayi

Chorea - a ... Chorea a yara. rheumatic chorea

Chorea - a Pathology na juyayi tsarin. Yana nufin siffofin hyperkinetic. Cutar da ake tare da matsalolin da cerebral subcortical nodes. Yana iya gano halayyar siffofin: wani episodic, aimless, m twitching na hannuwana da ƙafafuna, wani lokacin a cikin akwati. A baya, saukarwa akwai na hankali da ilimi nakasa, da matsaloli tare da daidaituwa, da kuma kai-da sabis. Yara chorea ne sau da yawa kuskure ga al'ada aiki ya karu. A gaskiya, a lokacin da farko alamun cutar bukatar neman m taimako.

Kalmar "chorea"

Kalmar da aka yi amfani da biyu lokuta. Yana iya nuna a fakaice m cuta, wanda kasance a wannan kungiya (msl, karamin Huntington ta chorea ko chorea). Har ila yau, shi ne amfani da su bayyana wasu syndromes cewa faruwa a lokacin da daban-daban na cututtuka. The kalmar "chorea" ya zo daga Girkanci harshe, inda aka nuna ta wani irin dance. Wannan bayyana farko bayyanar cututtuka, wanda bayyana kansu a cikin m, uncoordinated, jerky, m ƙungiyoyi daga cikin akwati da kuma extremities. The hali na haƙuri ne da gaske kamar involuntary, m dance. Da zarar kan wani lokaci kira chorea "St. Vitus ta dance." Wannan sunan yana da alaka da tsoho imani na St. Vitus, wanda aka rayayye yada Kristanci, wanda ya sa aka azabtar da shi da sojojin Roma. Bayan mutuwarsa ya zama mashahuri labari cewa idan wani yin wani aiki dance a kusa da kabari a kan ranar haihuwar, zai samu wani cajin na vivacity da makamashi na dukan shekara.

dalilai

A Sanadin cutar iya daban-daban asalin, amma mafi yawa chorea sa hereditary dalilai ko kwayoyin cuta.

Kadan na kowa chorea, lalacewa ta hanyar irin wannan dauke da kwayar cutar yanayin cututtuka kamar cutar tarin fuka meningitis, kwayar encephalitis, neurosyphilis, Lyme cuta, whooping tari. Aukuwa na chorea iya dangantawa da rayuwa hanawa (idan akwai wani Fabry ta cuta, hyperglycemia, hyperthyroidism, ko Wilson ta cuta), intoxications (guba baka hana, Mercury, lithium, digoxin, neuroleptics, levodopa), autoimmune pathologies (kamar antiphospholipid ciwo , tsari lupus erythematosus, mahara sclerosis). Daga cikin dalilan da cewa tsokana da ya faru da cutar, likitoci ma kira lalacewar kwakwalwa Tsarin. Wadannan sun hada da ƙari samuwar, hypoxic encephalopathy, traumatic kwakwalwa raunin, shanyewar jiki.

Common bayyanar cututtuka

Chorea - wata cuta da cewa bayyana kanta bazuwar, m, gajere jiki ƙungiyoyi. A wasu lokuta, waɗannan ƙungiyoyi da za a iya dauka a matsayin al'ada, isassun, hali mai lafiya da mutum, wani abu m. A wasu, sun kama wani tunanin, wanda ba a iya lura da shi ba dance. Jerky fizge iya zama wani daya- ko biyu-gefe, amma ba su sami a kalla wasu irin synchronicity.

Dangane da abin da aka samu wani nau'i na Pathology, rarrabe bayyanar cututtuka na chorea. Idan wani mutum dan kadan furta trochaic hyperkinesis, sa'an nan hali an kiyaye motor qananan damuwa, tare da motor disinhibition, ta ƙara emotionality, da wasu mannerisms, fidgeting, bai dace ba gestures.

Wadansu siffofin bayyananne kamar yadda chorea ƙungiyoyi peculiar "yo-yo". Mai tsanani nau'i na trochaic hyperkinesis tarwatsa motsi na tafiya, magana da kuma fuska. haƙuri da Gait ne ba kawai m, amma kuma a wasu awo "wawa". Chorea, da bayyanar cututtuka da wanda suna da matukar wuya, ba damar ko yin wasu ƙungiyoyi. Marasa lafiya da tsanani cuta ne dogara a kan su yanayi, kamar yadda ba ya motsa da kuma iya shirya kanka a rayuwa sosai.

Huntington ta chorea

Wannan Pathology bayyana kanta a mafi yawan lokuta dake da shekaru 35 zuwa shekaru 45. Chorea, da bayyanar cututtuka na wanda, a Bugu da kari ga hankula hyperkinetic, kawo mafi hali cuta da gigin-tsufa (dakushe m) tasowa sannu a hankali, wani lokacin wuya a gano, lokacin da shi ya fara bayyana. A farko m ƙungiyoyi yawanci faruwa a kan fuskarsa. Su za a iya rikita batun tare da bazuwar motor automatisms (wannan protruding harshe, frowning, lasawa lebe, baki bude). Ci gaban da cutar da aka bayyana a cikin ci gaban hyperkinetic a cikin akwati, kuma extremities. Mai tsananin form halin da ciwon na magana, memory, hadiya tsari, da matakin na kai-da sabis da kuma ƙare da gigin-tsufa. Fara for Huntington ta chorea ne shafi tunanin mutum da cuta a cikin nau'i na hallucinatory-paranoid, affective da kuma halayya cuta.

Neyroakantotsitoz

Neyroakantotsitozom marasa lafiya sha ba kawai trochaic hyperkinesis, amma acanthocytosis (canje-canje samar da ja da maikacin jini). Ya bambanta da alama a wannan Pathology ne atrophy (mãsu rauni a tsokoki na manya da ƙananan extremities). Daga cikin wasu halaye rarrabe cututtuka: baka hyperkinesis da taban da ake ƙungiyoyi, jerking lebe protruding harshe da kuma sauran fuskoki. Lokacin da neyroakantotsitoze haƙuri involuntarily iskusyvaet harshensa, lebe da kuma tsiraita ga ciki surface na jini. A complicating factor a wannan cuta da kuma gigin-tsufa protrude seizures.

Cuta Lesch-Nai Han

Nakasar cututtuka na juyayi tsarin tsoma baki tare da wani mutum ya rayu cikakken rai. Wadannan pathologies alaka cutar da kuma Lesch-Nai Han. A primary hanyar cuta ne a hereditary rashi na hypoxanthine-Bibyun. Wannan chorea a yara yana tare da tsanani disturbances a cikin aiki na juyayi tsarin. Har ila yau, Pathology tsokani karin samar da uric acid.

Daga cikin watannin farko na rayuwa da yaron ya gani wani bata lokaci ba, a ci gaba. A rigidity da wata gabar jiki da aka nuna a cikin watan uku. Daga shekara ta biyu ta rayuwa da jariri da ciwon fuska grimaces, wanda suna tare da ãyõyin pyramidal fili raunuka da kuma jinkirta shafi tunanin mutum da ci gaba. Baby iya jiki cutar da kansu ne da cizon bakinsu, ko yatsunsu.

benign chorea

Yãfẽwa Chorea a yara bayyana kanta a cikin ƙirjinka ko farkon yara. Pathology tana nufin hereditary cututtuka. Jimlace hyperkinesia a wannan cuta retreats kawai a lokacin da jariri tana barci. Daga Huntington ta chorea, irin wannan Pathology ne daban-daban wadanda ba progressors da kuma al'ada ci gaban m. A mazan shekaru a benign chorea Za ka iya rage hyperkinetic, idan lokacin da za a tuntube da likita makaman.

Secondary siffofin chorea

Mafi na kowa sakandare siffofin cuta suna dauke biyu: chorea da chorea ciki.

A farko an kira Sydenham ta chorea. Ta bayyanar iya tsokana m streptococcal kamuwa da cuta, ko rheumatic zazzabi. M irin halin da karin gishiri grimace, ma'ana gestures, ƙungiyoyi disinhibition. More hadaddun siffofin trochaic hyperkinesis bayyana a gaskiyar cewa haƙuri wuya a motsa, magana kullum, ko numfashi. Lokacin da cutar na faruwa kamar yadda "tonic" gwiwoyi da "curable" reflexes, wani tunanin da kuma affective cuta, murdede hauhawar jini.

Ciki chorea - wata cuta da cewa an koma daga ƙuruciyarsa. Wannan shi ne, a cikin hadarin zone, sũ ne waɗanda mata suka ci karo da wani yaro da kananan mawaka. Pathology iya faruwa a lokacin farko ciki domin 2-5 watanni. A m Hakika na "ban sha'awa" halin da ake ciki kuma iya bayyana chorea. Jiyya a irin haka ne m, a matsayin cutar vuya da kanta bayan wani katsewa na ciki ko bayan haihuwa.

chorea rheumatica

Abin da ya faru da cutar zo a tsakiyan heightened rheumatic zazzabi ko endocarditis, wanda yana tare da valvular cututtukan zuciya. Lokuta da dama da cutar ba related to wannan factor, da kuma cutar bayyana kanta da kansa.

Rheumatic chorea mafi sau da yawa rinjayar yara dake da shekaru 6 da shekaru 15. A 'yan mata, da Pathology ne fiye da na kowa. A mataki na farko da cutar na iya zama wani dalilin damuwa, saboda bayyanar cututtuka an iyakance ga grimaces, kuma iyãyensa dauke shi a matsayin wani wargi. Kan aiwatar da kananan involuntary ƙungiyoyi daga cikin wata gabar jiki, da suka fara da yatsun kafa kuma sannu a hankali yada a ko'ina cikin jiki. A mako daga baya ya zo da zanga-zanga lokacin, a lokacin da yaro ya ƙungiyoyi masu azumi da kuma gaggarumar. Wannan yanayin ya hana jariri don ci gaba da al'ada ake gudanar, cewa shi ne, don ya ci, ya yi tafiya, to rubuta.

Rheumatic chorea ya tarwatsa wani yaro ta fuska tare da dubban grimaces. M siffofin da cutar tsoma baki tare da mãsu haƙuri a tsaya, ya hadiye, to magana, da kuma jiki ne kullum motsi. Idan kamu da chorea, magani ya kamata a za'ayi sosai da kuma gaggawa.

bincikowa da

Mayakan chorea bayyana saboda m hali. A wani na farko jarrabawa, likita dole rike wani zance da haƙuri ko iyalinsa. A musamman yana da muhimmanci a san ko rashin lafiya wani a cikin iyali da wannan cuta, da yadda suka yi tsawo chorea bayyanar cututtuka, ko haƙuri ya dauki kwayoyi, ko kumburi cututtuka sha wahala. Bugu da ari gwani dole ne tantance involuntary ƙungiyoyi. Haka ma wajibi ne don yin bincike da kuma bayanin cututtuka da za a iya tare da chorea, sa tsanani ilimi karkacewa. Bayyanar cututtuka na wadannan cututtuka ba ko da yaushe ne bayyananne. Wani lokaci, domin gane irin munanan a wani wuri mataki, wani hadadden ne da za'ayi safiyo. A jini gwajin zai nuna da matakin jan a cikin jini da kuma gaban ko babu alamun kumburi halayen. Bugu da kari, gudanar da kwamfuta tomography, Magnetic rawa Dabarar, electroencephalography.

magani

Chorea - a Pathology cewa ba da damar da haƙuri da su gudanar da saba cikakken rai, don haka ya kamata a bi da a dace da m. Daban na magani ya dogara da cuta-haddasa dalilai. Alal misali, a Wilson ta cutar haƙuri An wajabta a rage cin abinci tare da m abun ciki na tagulla da kuma kwayoyi wanda mataki ne directed a rage ta sha.

Chorea Huntington wajabta neuroleptics da benzodiazepine tranquilizers. Idan chorea sa ta na kullum insufficiency na cerebral jini ya kwarara, a can ne bukatar da kwayoyi da runtse jini. Vasculitis kwashe hormonal magani. Idan ka bayyana sosai kowa yana da cututtuka, magani ya kamata a hadaddun.

Rage tsanani da involuntary ƙungiyoyi ne zai yiwu, ta hanyar m baki, a lokacin da ya hallakar da ventrolateral tsakiya na thalamus. Chorea bukatar daukar kwayoyi da inganta aiki na kwakwalwa da kuma abinci mai gina jiki, kazalika da bitamin na kungiyar B.

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