Kiwon lafiyaCututtuka da kuma Yanayi

Dandy Walker ciwo: yanayi na abin da ya faru, cututtuka, magani da kuma hangen nesa siffofin

A halin yanzu, haske ya bayyana da yawa yara haife tare da wata cuta. Daya daga cikin mafi hadaddun da tsanani da rikitarwa ne Dandy Walker ciwo.

Babban Sanadin nakasar munanan wadannan:

  1. Mafi yawa daga cikin masana da'awar cewa shi ne wani hereditary cuta, wadda aka genetically m. Wannan ya tabbatar da samuwa a cikin likita kimiyya statistics.
  2. Dandy Walker anomaly 'ya'yan mafi sau da yawa yakan faru a cikin wadanda uwayensu suka sha wahala daga matsananciyar shan barasa. Kuma, na iya zama ba ya nan ko da sauran related kayyade munanan a yaro. Baya da cewa jiki na mata da suka sha ba m yanayi ga ci gaban da tayin, wani contingent sau da yawa daukan sosai m for hali. Saboda haka, Dandy Walker ciwo a wani yaro da aka fi sau da yawa ya gano kawai bayan haihuwa.
  3. Genetically-sa ciwon sukari, rubella, cytomegalovirus kamuwa da cuta a cikin mata masu ciki - shi ne ma hadarin dalilai domin ci gaba da wannan anomaly.

Dandy Walker ciwo za a iya gano ta hanyar da wadannan cututtuka.

A farko alamun yana yiwuwa a gano a cikin ashirin da biyu makonni. A duban dan tayi jarrabawa ne riga pathognomonic, hankula bayyanar cututtuka, da suka hada da:

  • gaban cysts a yankin na fossa (yanki manyan tankuna)
  • aplasia ko hypoplasia na cerebellar vermis.
  • kara girman hudu ventricle.

A kan ya fi girma mataki na ciki ta bayyana, kuma a bayyane cututtuka:

  • "Kogon palate" .
  • "Tsattsãgẽwa lebe".
  • nakasar koda anomalies.
  • syndactyly - Fusion na yatsunsu a kan wata gabar jiki.

Dandy Walker ciwo fara fito fili da sauri bayan haihuwa. Wannan Gaskiya ne, mai tsanani neurological bayyanar cututtuka, mai tsanani daga shi ne m. Very da sauri, ãyõyi a matsayin intracranial hauhawar jini da kuma hydrocephalus.

A yaron tare da wannan Pathology ne sosai m, aka lagging a baya a ci gaba, duka biyu jiki da kuma Psycho-neurological. cerebellar cututtuka ma generated - daidaituwa cuta, spastic tsoka yanayin da ataxia.

DendiUokera ciwo. Magani da kuma ganewar asali

Sirri na prenatal ganewar asali - " 'ya'yan Dandy Walker ciwo" - a gaban mahaifinsa da mahaifiyarsa yana sanya wani sosai tsanani matsala. Kana bukatar ka yanke shawara - don ci gaba da kuma ba da 'ya'ya tare da kashi 100 Yiwuwar wani rashin lafiya yaro, ko da daukar ciki da aka kare. Yawancin lokaci, likitoci bayar da shawarar da na biyu zaɓi.

Duk da wannan, yara tare da wannan nau'i na cuta, ana haifuwarsu kullum. Jiyya a cikin wannan yanayin ne ƙwarai da gaske, kuma shi ne yawanci m.

Amma tiyata da aka yi amfani da lokacin da wani bai cika form na Pathology da hydrocephalus. Dauke da kewaye a kaikaice ventricle da mafitsara ba zai iya kawar da kwakwalwa lalacewa. The yaro zai girma neuropsychiatric naƙasasshe tare da m jiki rikitarwa, mai yawan hade cututtuka, da hankulansu rashi.

Forecast na ci gaba yara tare da wannan anomaly

Forecast na ci gaba da yara suka yi Dandy Walker ciwo yana gyarawa, sosai ya fi karfinsu. Matsayin mai mulkin, a hankali kara cerebral decompensation. A wannan yanayin, idan akwai mai tsanani nau'i na cutar da kuma rashin dace asibiti kallo, da irin wannan haƙuri mutu a watanni shida na farkon rayuwarsa. Bisa kididdigar da, shi ne hamsin cikin dari.

Sauran yara, har idan akwai wani tsanani aiki na likitoci da kuma iyãyensa ne sosai a baya a ta ci gaba, tun da matakin na hankali suna da wani sosai low (ba tare da yiwuwar warke shi daga baya a kan). Bugu da kari, akwai wata alama aikin neurological matsayi.

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