Kiwon lafiyaCututtuka da kuma Yanayi

Fused yatsun: Sanadin kuma Jiyya

Me wasu jarirai, ana haifuwarsu Fused yatsun kafa? Menene wannan Pathology, da kuma ko za ka iya rabu da shi? Amsoshin wadannan da sauran tambayoyi game da sabawa ambata kayan za ka koya daga wannan labarin.

Janar bayani game da Pathology

Fused yatsun kafa - wani nakasar ƙananan reshe ci gaba. Wannan sabawa ne halin da m ko cikakken Fusion na biyu ko fiye yatsunsu. A likita yi, Fused yatsun kafa da musamman sunan - syndactyly.

Tare da wannan cuta a cikin mutane na iya zama wani Fusion na biyu maras kyau da kuma underdeveloped yatsunsu kuma yadda ya kamata ci gaba. A sakamakon syndactyly ne aikin da kwaskwarima lahani daga cikin ƙananan reshe.

The yaro da sabawa kamata ko da yaushe a shawarci wani halitta kuma an orthopedic likita. Don saita da irin syndactyly, kamata a da za'ayi X-ray na ƙafa. Jiyya wannan aibi aka yi kawai da aikin tiyata. A wannan yanayin, biyu Fused yatsun kafa suna rabu da amfani da roba da kuma aibi ƙulli a lokacin da cikakken zama dole.

wasu statistics

Syndactyly kira mahaukaci ci gaban da yatsunsu, wanda shi ne sakamakon wani warwarewarsu da dama na rabuwa. Yawanci, wannan na faruwa a lokacin da amfrayo lokaci.

Fused yatsun kafa na wani jariri da aka samu da wani mita na 1 zuwa 3000. Ya kamata a lura cewa syndactyly ne game da rabin dukkan nakasar anomalies. Irin tafiya da ƙafãfu da Pathology iya zama ko dai mai zaman kanta deflection, kuma hadu da sauran lahani (msl, yatsunsu hypoplasia, polydactyly da polifalangiey, ectrodactyly, brachydactyly, brachioradialis synostosis, tsagawa goge, ulnar ko radial clubhand da sauransu.).

Kimanin 60% na yara da suka yi a Fused yatsun (photo lahani gabatar a wannan labarin), suna hade nakasar munanan a musculoskeletal tsarin (misali, pseudarthrosis, kwancen kafa, mahaukaci birki kafuwa, da dai sauransu).

hanyar da lahani

Me ya sa yara ci gaba da irin wannan mataimakin, kamar Fused yatsun kafa? A Sanadin wannan sabawa iya zama daban-daban. Masana sun yi imani da cewa a cikin 20% na lokuta wannan ne saboda da hereditary dalilai. A wasu kalmomin, duk laifi na wani autosomal rinjaye juna na gādo.

Idan wani iyali tarihi na syndactyly ya bace, dole ne a zaci cewa keta bambantawa da kuma samuwar na ƙananan wata gabar jiki da tayin faru a lokacin embryogenesis. Yawanci wannan ya faru a lokacin da akwai tasiri na daban-daban m dalilai.

A aibi tasowa?

Me kafafu Fused yatsunsu, da kuma yadda za a bayyana irin wannan reshe inganta? ba a haifa ba baby kafar shafin ya auku a 5th mako na intrauterine ci gaba. Sai a wannan lokaci a cikin tayin iya ci gaba physiological syndactyly.

A babu wani aibi riga a cikin 7th mako na yatsunsu suna kafa. Wannan shi ne saboda ci gaban da yatsa haskoki da kuma rage cin gaban interdigital sarari. Idan rage daga cikin interdigital ganuwar karya, sa'an nan da phalanx ba a rabu, cewa shi ne, akwai syndactyly.

Yiwu haddasawa mahaukaci cin gaban

Fused yatsun kafa, da yaro zai iya faruwa a mai guba effects a jiki na mace mai ciki. A mafi yawan lokuta wannan ya auku a lokacin shan magani, giya, kazalika da ya fi karfinsu da lafiyar qasa, siffofi da sana'a, X-ray sakawa a iska mai guba da kuma cututtuka (msl, mura, syphilis, da tarin fuka, da dai sauransu).

Sau da yawa Sanadin haihuwa na wani jariri da syndactyly kasance m.

Fused yatsun kafa - shi ne sau da yawa kiyaye aibi cikin tsarin chromosomal da kwayoyin syndromes.

Af, aka sosai da wuya samu a cikin mutane samu syndactyly. Yawanci, irin wannan Pathology taso bayan kafa konewa (thermal ko sunadarai).

Fused yatsun kafa - wanda ke nufin da wannan Pathology?

Mutane da yawa waɗanda rayayye a kai asiri, an yi imani da cewa wannan Pathology tasowa ba kawai. An yi imani da cewa irin wannan maye gurbi ne diabolical. Lalle ne, Fused yatsu ne quite reminiscent na kofato.

Duk da haka, likitoci sun ce kome m, kuma m, a da cewa kafar ba ci gaba. Wannan shi ne kawai wani anomaly reshe, daga abin da mai sauki ne ya rabu da mu, musamman a farkon matakai na yaro ta rayuwa.

Saboda haka kada ku damu sosai, idan ka kasance Fused yatsun kafa. Menene wannan yake nufi, za ka iya ce kawai wani likita, ba wani diabolical masoya tasirin.

rarrabuwa na lahani

A orthopedics syndactyly graded bisa ga tsawon, da irin kabu, kazalika da jihar na yatsunsu.

A halin yanzu bambanta:

  • kashi siffar (a lokacin da kashi karu auku).
  • taushi nama form (wani lokacin membranous da kuma fata).

lahani rarrabuwa tsawon dogara da yawan da kuma tsawon phalanges Fused kabu.

Game da jihar Fused yatsunsu, da syndactyly iya zama hadaddun da sauki. A karshen harka akwai wani Fusion na al'ada yatsa, da kuma a cikin na farko - da munanan daga kashi, hadin gwiwa, agara ko jijiya na'ura.

kwayoyin iri

Syndactyly classified da kuma kayyade iri:

  • Nau'i na farko - zigodaktiliya. M ko cikakken fe (membranous) 2nd da 3rd kafana. Har ila yau, ba zai yi jinyar sauran webbed yatsunsu.
  • Nau'i na biyu - sinpolidaktiliya. Fusion na 4th da kuma 5th yatsun tare da cire tallafin 5th. Domin wannan Pathology ne halin da: a take hakkin reliefs fata tafin kuma hypoplasia na tsakiya phalanx.
  • The uku type. Bangarorin cikakken syndactyly na 4th da kuma 5th yatsunsu. A wannan yanayin, da kafa ba ya canzawa.
  • A karo na hudu irin - syndactyly Gaza. Cikakken hadin cutaneous syndactyly hannunka. A lokaci guda akwai wani tasha hasãra.
  • A karo na biyar da irin. Ci yatsun kafa da kuma metacarpal ƙasũsuwa. A cikin hannãyen ne fiye da na kowa 3-4 Fusion na yatsunsu da sãwãyensu - 2 da kuma 3.

lahani cututtuka

Lokacin da syndactyly na ƙafa a wani yaro da aka fi sau da yawa ya lura Fusion na 2nd da 3rd yatsun kafa. A daidai wannan m phalanx iya zama ko dai underdeveloped ko ɓullo da kullum. A wasu lokuta, akwai wani karu a yawan yatsunsu, saboda su amniotic yanki.

Ba kamar yara tare da syndactyly a hannun yara da syndactyly ƙafafun ci gaba quite al'ada. Bã su da wani matsaloli tare da aiwatar da fadi da kewayon ayyuka. A wannan aikin rashi na kafar ba ya kawo cikas da karatu, kazalika da kusan ba ya takaita da zabi na gaba sana'a.

Yadda za a gane asali?

Yadda za a gane asali Fused yatsun (da wata ãyã cewa irin aibi da aka bayyana kawai a sama)? Syndactyly gano neonatologist nan da nan bayan haihuwar jariri. Bugu da ari kallo na yaro ne da za'ayi na yara orthopedics ko tiyata. Don ware chromosomal kuma gene munanan za a iya haɗa da wani tsarin halittar jini.

Duk da cewa irin wannan ganewar asali da aka sanya bayan wani gani dubawa don bayyana da irin aibi, kazalika da ci gaba da magani dabarun, shi wajibi ne su gudanar da wani binciken kayan aiki.

Radiography kafa a biyu tsinkaya damar masana don kimanta da yawa daga kashi, hadin gwiwa kiwon lafiya, da tsawon da kuma gaban kashi fe. Don gane da halaye na jini ya kwarara da kuma jijiyoyin bugun gini na cibiyar sadarwa a yatsunsu yi UZDG, reovasography, angiography da lantarki ma'aunin zafi da sanyio.

cuta magani

Shin, akwai wani mai magani Fused yatsun kafa? Operation ka raba da phalanges - wannan ne kawai zai yiwu bayani. Duk da haka, ya kamata a lura da cewa m hanya da ake amfani kawai idan syndactyly na da yatsunsu. Game da Fused phalanges daina, sa'an nan da aiki ba da aka nuna. Idan irin wannan abnormality tsarè al'ada tafiya, da baki ne har yanzu da za'ayi.

Lokacin da aiki da yake faruwa a?

Sharuddan kuma Hanyar daga m baki aka ƙaddara dangane da yanayi da kuma siffar da lahani. Manufar wannan magani ne da ya kawar da kwaskwarima aibi, kazalika da inganta aiki da kafar ko hannunsa.

A ganiya lokaci domin aiki - da shekaru 4-5 shekaru. Idan wani jariri da aka kiyaye syndactyly karshen, da baki ne da za'ayi a karo na biyu rabin ransa. Wannan ya hana nakasawa na sakandare yatsunsu da m girma na phalanges.

m kusance

A lokacin m ayyukan da wadannan fuskanci iya amfani da:

  • rabuwa da conjoined yatsunsu tare da fata plasty tare da na gida kyallen takarda.
  • membranous rabuwa kabu skinless robobi.
  • Fused rabuwa yatsunsu, wanda aka complemented hada da yin amfani da fata grafting tare da free autografts da kuma gida kyallen takarda.
  • rabuwa da conjoined yatsunsu, wanda aka complemented free fata grafting polnosloynym ko tsaga fatar jiki dasa.
  • multistage tsangwama tare agara-tsoka, fata da kuma kashi grafting.

A postoperative zamani

Bayan tiyata don immobilize da raba yatsunsu a kan wani reshe gabatar da wani m plaster karan ɗori. An shawarar sa a kalla 3-4 watanni.

Aƙalla kwanaki 15 bayan da aiki a fara da haƙuri ta dawo. Don yin wannan, amfani da tausa hannu ko ƙafa, motsa jiki far, phonophoresis da Lydasum, lantarki ruri na tsokoki na yatsunsu, ozokerite, paraffin da laka wraps.

A sakamakon da aiki

Hanyoyin amfani da zamani a tiyata magani daga syndactyly ba kyau kwaskwarima da kuma aikin da sakamakon. Tare dace baki ne gaba daya mayar ba kawai al'ada tsari, amma kuma da buroshi aiki na ƙafa.

Surgery cire syndactyly ta yi nasara idan haƙuri yana da wani tightening scars da kuma a kaikaice nakasar yatsunsu, kuma akwai cikakken kewayon motsi a interphalangeal hadin gwiwa (adduction, sata, tsawo da kuma lankwashewa), fahimtar aiki (a cikin hali na goga), mai kyau ƙwarai da na halitta nau'i da sarari tsakanin yatsun kafa.

Idan da magani daga syndactyly yanke shawarar ba a gudanar da wani, tana iya samun mummunan tasiri a kan ci gaba da kuma ci gaban da jaririn wata gabar jiki.

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