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Raunin Recklinghausen shine irin ni neurofibromatosis

Neurofibromatosis - cututtuka da bayyanar da ciwon sukari akan jikin mutum. Wadannan cututtuka sune hade kuma suna hade da wasu abubuwan da suka faru a cikin kwayoyin. Ko da yake akwai nau'o'in neurofibromatosis da dama, labarin zaiyi la'akari da nau'in farko - cutar Recklinghausen, wanda masana kimiyya suka fara bayani a karni na 19. Ka yi la'akari da bayyanar cutar, abubuwan da suka haifar da hanyoyin maganin.

Yaya aka nuna cutar ta Recklinghausen?

Wani mutum mai wahala irin na Niurofibromatosis (NF1) an riga an haife shi tare da wannan cuta, amma cutar bazai iya da'awar shekaru ba. Neurofibromatosis (cutar Recklinghausen) a kowane mutum yana nuna kansa a hanyoyi daban-daban. Kwayoyin cututtuka suna da saukin kamuwa da maza da mata.

Idan mai haƙuri yana da NF1, to, yawancin akwai alamun bayyanar kamar su:

  • Ƙunƙasar launi na kofi da launi mai tsabta akan fata;
  • Ƙwararrun marasa ci gaba a sama ko žasa da fata.

Kusan kashi daya bisa uku na marasa lafiya da cutar Recklinghausen kuma suna shan wahala daga wasu matsalolin lafiya. Wadannan sun haɗa da:

  • Hawan jini;
  • Spine mai launi (scoliosis) ko cututtuka a wasu ƙasusuwa;
  • Matsalolin tunani na yiwuwa;
  • Matsaloli da hali;
  • Glioma na jijiyoyi masu jiji;
  • 10% da marasa lafiya da fuskantar m ƙari membranes na gefe jijiya (mesenchymal marurai), wanda na iya faruwa a lokacin rayuwar.

Me yasa Cututtukan Recklinghausen ke faruwa?

Kamar yadda aka fada a sama, rubuta ni neurofibromatosis shine cututtuka wanda ke haifar da maye gurbin wani taswirar jinsi a cikin mutum 17 na mutum. A sakamakon haka, ci gaba da rashin ci gaba da ciwon sikila ya faru.

Fiye da kashi 50 cikin dari na cututtukan Recklinghausen (hotuna da aka gabatar a cikin labarin) ana daukar su daga iyayensu ga yaro. Duk da haka, akwai lokuta a yayin da abin da ke faruwa na NF1 yana hade da kariyar jigilar mutane a cikin mutane. Ana kiran wannan maye gurbi.

Akwai gwaje-gwaje da ke taimakawa wajen gane cutar Recklinghausen a cikin yaron da yake cikin cikin mahaifa. Duk da haka, a mafi yawan lokuta, cutar za a iya bincikar cutar ne kawai bayan haihuwa.

Yaya Aka Yi Amfani Da Cututtukan Recklinghausen

Magunin bai riga ya shirya don bada amsa ga wannan tambaya ba - an gano magungunan magani mai kyau. Idan mai haƙuri ya nuna cutar Recklinghausen, to dole ne ya kasance a karkashin kulawar likitoci. Kuma idan cutar ta haifar da barazana ga rayuwa (wanda ya faru ba tare da dalili ba) saboda shan kashi na kwaya, likitoci zasuyi aiki don kawar da wannan hatsari.

Cutar cutar Recklinghausen ba ta da magani kawai. A wannan yanayin, ana kawar da ciwace-ciwacen ƙwayoyi, an yi ƙoƙari don kawar da ƙwayoyin cuta a kasusuwa. Bugu da ƙari, an wajabta magunguna don magance wasu matsalolin lafiya na iya haifar da NF1. Idan akwai ƙwayar ci gaba fiye da ɗaya akan jikin mutum, da kuma yawan ciwon sukari, to, mafi yawan lokuttan x-ray ne aka tsara. Binciken nagari da kuma dacewa da kyawawan lokuta suna taimaka wa mutane su rayu cikin rayuwar da ta dace.

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